A female case report of benign recurrent intrahepatic cholestasis with hepatitis A.
نویسندگان
چکیده
منابع مشابه
Recurrent intrahepatic cholestasis of pregnancy. A case report.
Intrahepatic cholestasis of pregnancy (ICP) represents a rare but severe pathology with serious consequences on the outcome of pregnancy. We present the cases of two sisters that came to our clinic with ICP in successive pregnancies. The fetus from a pregnancy with cholestasis can be affected by preterm birth, respiratory distress syndrome, intrauterine death in the third trimester and a possib...
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Benign recurrent intrahepatic cholestasis (BRIC) is a rare autosomal recessive inherited disorder characterized by multiple recurrent episodes of severe cholestatic jaundice without obstruction of extrahepatic bile duct. We present the case of a 7-year-old boy with BRIC confirmed by mutation analysis in the ATP8B1 gene and typical clinical manifestation. Despite inheritance of BRIC, we detected...
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ژورنال
عنوان ژورنال: Kanzo
سال: 1991
ISSN: 0451-4203,1881-3593
DOI: 10.2957/kanzo.32.932