منابع مشابه
Lhermitte-Duclos Disease (Dysplastic Cerebellar Gangliocytoma) in a Young Patient
Lhermitte Duclos disease also called dysplastic gangliocytoma of cerebellum is an extremely rare cerebellar neoplasm. It usually presents with raised intracranial pressure along with cerebellar signs. We report a rare case of Lhermitte Duclos disease of a 20 years male who presented with signs & symptoms of raised intracranial tension. CT features were suggestive of Lhermitte-Duclos disease. Su...
متن کاملAcute Hydrocephalus Revealing Unusual Cerebellar Mass: Dysplastic Cerebellar Gangliocytoma or Lhermitte-Duclos Disease (LDD)
Lhermitte-Duclos disease (LDD) or dysplastic gangliocytoma of the cerebellum is a rare benign lesion of uncertain pathogenesis characterized by overgrowth of cerebellar ganglion cells which replace granular cells and Purkinje cells; this results in gross thickening of the cerebellar folia. It is revealed by symptoms of raised intracranial pressure, cerebellar impairment and obstructive hydrocep...
متن کاملAssessing a Dysplastic Cerebellar Gangliocytoma (Lhermitte-Duclos Disease) with 7T MR Imaging
Lhermitte-Duclos disease (LDD; dysplastic cerebellar gangliocytoma) is a rare hamartomatous lesion of the cerebellar cortex and this was first described in 1920. LDD is considered to be part of the autosomal-dominant phacomatosis and cancer syndrome Cowden disease (CS). We examined the brain of a 46-year-old man, who displayed the manifestations of CS, with 7 Tesla (T) and 1.5 T MRI and 1.5 T M...
متن کاملAcromegaly associated with gangliocytoma.
BACKGROUND Acromegaly secondary to growth hormone-releasing hormone (GHRH) excess is rare. AIMS/CASE DESCRIPTION We report two patients with acromegaly who were diagnosed with sellar gangliocytomas that were immunopositive for GHRH. Tumour tissue persisted after debulking surgery and in the second case this was associated with persistent growth hormone hypersecretion, successfully suppressed ...
متن کامل[Non-functioning gangliocytoma of the pituitary gland].
Pituitary gangliocytomas are uncommon benign tumors (less than 100 cases have been reported to date)1-6 with a low proliferation potential and a slow growth. Histologically, most pituitary gangliocytomas are mixed tumors consisting of neuronal ganglion cells and an adenomatous proliferation of adenohypophyseal cells4,7,8; both components may occur as a single nodule or coexist as separate but a...
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ژورنال
عنوان ژورنال: Neurologia medico-chirurgica
سال: 1964
ISSN: 0470-8105,1349-8029
DOI: 10.2176/nmc.6.110