307 Are the UK Cystic Fibrosis Trust recommendations for bone health achievable?

Report of the UK Cystic Fibrosis Trust Bone Mineralisation Working Group

Maintaining Respiratory Health in Cystic Fibrosis Patients

Cystic fibrosis (CF) is an inherited disease that primarily affects the lungs and the digestive system, however, it also affects a number of other organs and systems. More than 90% of mortality of  CF patients is due to lung complications.  Healthy lungs are important for a long life for people with CF, We will discuss two important topics for maintaining respiratory health. Chronic use of drug...

Bone Mineral Density and Cystic Fibrosis: A Review

Cystic fibrosis (CF) is a common progressive genetic disorder among children which involves lungs, kidneys, intestine and liver. Apart from the significance of genetic factors, various environmental factors particularly bone mineral density are directly associated with CF. Remarkably, bone disease is appeared as a routine and commo...

Guide to bone health and disease in cystic fibrosis.

Cystic fibrosis (CF) is the most common genetic disease within the Caucasian population and leads to premature respiratory failure. Approximately 60,000 individuals are currently living with CF in North America and Europe, 40% of whom are adults. The life span of these patients has increased from approximately 2 to 32 yr of age over the last three decades. Bone disease has emerged as a common c...

Cystic Fibrosis Related Bone Disease

22 Context: Young adults with cystic fibrosis (CF) are at risk for low bone density and fractures, but the 23 underlying alterations in bone microarchitecture that may contribute to their increased fracture risk are 24 currently unknown. 25 Objective: The main goal of this study was to utilize high resolution peripheral quantitative computed 26 tomography (HR-pQCT) to characterize the bone micr...