une angiomatose diffuse cortico-méningée non calcificante et une démyélinisation progressive de la substance blanche. J Neurosurg 1946; 9:42–54. 6. Gururaj AK, Sztriha L, Johansen J, Nork M. Sturge-Weber syndrome without facial nevus: a case report and review of the literature. Acta Paediatr 2000;89:740–743. 7. Ward JB, Katz NN. Combined phakomatoses: a case report of SturgeWeber and Wyburn-Mas...

Purpose/background: Concomitant intraocular and orbital space-occupied lesions are relatively rare and this is the first report stressing the underlying causes of concomitant intraocular and intraorbital lesions. In this paper, we present cases showing both intraocular and orbital soft tissue masses and highlight their clinical, pathological and imaging features. Materials and methods: A retros...

This study presents the results of a rehabilitation program in a spastic hemiparetic subject who had undergone hemispherectomy because of SturgeWeber syndrome and intractable epilepsy. Sturge-Weber syndrome includes unilateral cerebral cortical angiomatosis, which often leads to progressive cerebral dysfunction and epileptic seizures that are medically difficult to control. A three-year-old gir...

T he main abnormality of the uveal tract in patients with Sturge-Weber syndrome is diffuse choroidal hemangioma (DCH). Diffuse choroidal hemangioma can lead to a total retinal detachment and secondary neovascular glaucoma. Radiotherapy and photodynamic therapy are currently the preferred methods of treatment. Low-dose lens-sparing radiotherapy or proton beam irradiation can induce tumor regress...

1. Méndez T, Otero I, García R, Pérez B. Síndrome de Klippel-Trenaunay-Weber: presentación de un caso. Rev Cubana Oftalmol. 2001;14:47-9. 2. Bordel MT, Miranda A. Un caso atípico de síndrome de Klippel-Trenaunay. Piel. 2005;20:306-8. 3. Gimeno P, Pérez P, López-Pisón J, Romeo M, Galeano N, Marco M, et al. Síndrome de Klippel-Trenaunay: a propósito de tres nuevas observaciones. An Esp Pediatr. 2...

The fundamental abnormality in the SturgeWeber syndrome (SWS) is considered to be the lack of superficial cortical draining veins, which results in numerous collateral pathways of venous flow. Venous abnormalities have been described in detail using angiography but magnetic resonance imaging (MRI) has replaced angiography in the diagnosis of SWS. In this paper we aim to demonstrate the range an...