نتایج جستجو برای: lcad acetate

تعداد نتایج: 50100  

Journal: :acta medica iranica 0
gh. karimi a. khoshbaten. a.r. dehpour--. m. abdollahi m. sharifzadeh

effects of 28 days lead acetate (ioc, 500, 1000 ppm) treatment on hypertension ami relationship between blood lead levels and hypertension in male. spraguc-dawley rats were studied. results of this study showed tlxat lead acetate treatment did run decrease, body wcight or water consumption, except for lead acetate (1000 ppm) and sodium acetate (500 ppm) which increased fluid consumption when co...

Journal: :Proceedings of the National Academy of Sciences of the United States of America 1998
D M Kurtz P Rinaldo W J Rhead L Tian D S Millington J Vockley D A Hamm A E Brix J R Lindsey C A Pinkert W E O'Brien P A Wood

Abnormalities of fatty acid metabolism are recognized to play a significant role in human disease, but the mechanisms remain poorly understood. Long-chain acyl-CoA dehydrogenase (LCAD) catalyzes the initial step in mitochondrial fatty acid oxidation (FAO). We produced a mouse model of LCAD deficiency with severely impaired FAO. Matings between LCAD +/- mice yielded an abnormally low number of L...

Journal: :The Journal of biological chemistry 2014
Eric S Goetzman John F Alcorn Sivakama S Bharathi Radha Uppala Kevin J McHugh Beata Kosmider Rimei Chen Yi Y Zuo Megan E Beck Richard W McKinney Helen Skilling Kristen R Suhrie Anuradha Karunanidhi Renita Yeasted Chikara Otsubo Bryon Ellis Yulia Y Tyurina Valerian E Kagan Rama K Mallampalli Jerry Vockley

Long-chain acyl-CoA dehydrogenase (LCAD) is a mitochondrial fatty acid oxidation enzyme whose expression in humans is low or absent in organs known to utilize fatty acids for energy such as heart, muscle, and liver. This study demonstrates localization of LCAD to human alveolar type II pneumocytes, which synthesize and secrete pulmonary surfactant. The physiological role of LCAD and the fatty a...

Journal: :Cardiovascular research 2013
Adrianus J Bakermans Michael S Dodd Klaas Nicolay Jeanine J Prompers Damian J Tyler Sander M Houten

AIMS The aim of this animal study is to assess fasting-induced changes in myocardial substrate metabolism and energy status as a consequence of mitochondrial long-chain fatty acid β-oxidation deficiency, using magnetic resonance spectroscopy (MRS). METHODS AND RESULTS Carbon-13 ((13)C) MRS of hyperpolarized [1-(13)C]pyruvate was used to assess in vivo pyruvate dehydrogenase (PDH) activity in ...

Journal: :Circulation. Cardiovascular imaging 2011
Adrianus J Bakermans Tom R Geraedts Michel van Weeghel Simone Denis Maria João Ferraz Johannes M F G Aerts Jan Aten Klaas Nicolay Sander M Houten Jeanine J Prompers

BACKGROUND Lipotoxicity may be a key contributor to the pathogenesis of cardiac abnormalities in mitochondrial long-chain fatty acid β-oxidation (FAO) disorders. Few data are available on myocardial lipid levels and cardiac performance in FAO deficiencies. The purpose of this animal study is to assess fasting-induced changes in cardiac morphology, function, and triglyceride (TG) storage as a co...

Journal: :The Biochemical journal 2005
Naomi van Vlies Liqun Tian Henk Overmars Albert H Bootsma Willem Kulik Ronald J A Wanders Philip A Wood Frédéric M Vaz

In the present paper, we describe a novel method which enables the analysis of tissue acylcarnitines and carnitine biosynthesis intermediates in the same sample. This method was used to investigate the carnitine and fatty acid metabolism in wild-type and LCAD-/- (long-chain acyl-CoA dehydrogenase-deficient) mice. In agreement with previous results in plasma and bile, we found accumulation of th...

2017
Evan M. Lord Charles E. Riggs

Fa tty acids are the primary fuel source for cardiac tissue in both humans and animals. These become especially important during times of starvation and long bouts of exercise. Fatty acids are broken down into smaller, useable acyl-CoA subunits through a process called beta-oxidation. The first step in this process must be catalyzed by one of four acyl-CoA dehydrogenase enzymes depending on the...

Journal: :American journal of physiology. Heart and circulatory physiology 2017
Rami Al Batran John R Ussher

In the 20th century, our knowledge of posttranslational modifications (PTMs) and their impact on protein function/enzyme activity was largely confined to that of protein phosphorylation and their regulation via kinases and phosphatases. However, as our scientific tools have become more sophisticated, and as we have advanced our knowledge of cellular/molecular biology, which has further been aug...

Journal: :Development & reproduction 2023

The sea cucumber, Apostichopus japonicus, is one of the most valuable aquatic species. color body wall and appearance are important for value cucumbers. To examine expression pattern long-chain acyl-coenzyme A dehydrogenase (LCAD), nuclear distribution C-containing protein 3 (NUDCD3), receptor tyrosine kinase Tie-1 (TIE1), previously reported as differently expressed genes during pigmentation w...

2009
A. J. Bakermans S. M. Houten T. R. Geraedts M. van Weeghel K. Nicolay J. J. Prompers

Introduction A common clinical feature of inherited defects in the mitochondrial fatty acid β-oxidation (FAO) pathway is the presentation of cardiac abnormalities. Chronic energy shortage and accumulation of -possibly toxiclipid metabolites may be key contributors to the pathogenesis of hypertrophic cardiomyopathy in FAO disorders. Previous studies have shown that increased myocardial lipid con...

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