aortopulmonary window (apw) is a rare congenital malformation. it results from an incomplete division between the ascending aorta and the pulmonary artery. we describe a 26-year-old male, who presented with a grade ii exertional dyspnea and palpitations. echocardiography revealed an apw with an ascending aorta aneurysm. he underwent surgery under cardiopulmonary bypass without aortic cross-clam...

the most frequent congenital heart defects in the neonatal period are ventricular septal defects. ventricular septal aneurysms can rarely develop from an interventricular septal (ivs) defect in adults. we describe a 47-year-old man with an aneurysm in the ivs growing towards the right ventricle, which was confirmed by cardiac computed tomographic angiography and was missed by echocardiography.

Holt-Oram syndrome is an autosomal dominant disorder, characterised by skeletal abnormalities of the upper limb associated with congenital heart defect, mainly atrial and ventricular septal defects. Skeletal defects exclusively affect the upper limbs in the preaxial radial ray distribution and are bilateral and asymmetrical. They range from clinodactyly, absent or digitalised thumb, hypoplastic...

holt-oram syndrome is an autosomal dominant disorder, characterised by skeletal abnormalities of the upper limb associated with congenital heart defect, mainly atrial and ventricular septal defects. skeletal defects exclusively affect the upper limbs in the preaxial radial ray distribution and are bilateral and asymmetrical. they range from clinodactyly, absent or digitalised thumb, hypoplastic...

Aortopulmonary window (APW) is a congenital heart defect characterized by the presence of an abnormal connection between pulmonary artery and proximal part aortic arch directly above level semilunar valves. It one rarest cardiac defects (frequency 0.2–0.6 %). APW occurs as isolated lesion or in association with other anomalies such coarctation aorta, interrupted arch, tetra­logy Fallot, atrial ...

T HE MANAGEMENT of patients with congenital communications between the ascending aorta and the main pulmonary artery is a challenging problem, not only in the establishment of the correct diagnosis preoperatively, but in subsequent surgical treatment as well. Although often described as a rare malformation, aortopulmonary septal defect will probably be encountered in any large group of patients...

Background: Aortopulmonary window is a rare congenital heart defect resulting from a communication between the main pulmonary artery and the ascending aorta. Surgical closure is indicated in all patients with aortopulmonary window and should be performed at the time of diagnosis to prevent irreversible pulmonary vascular disease. Methods: From 1990 to 2002, 4 infants with aortopulmonary window ...

Interrupted aortic arch is a rare congenital malformation of the aortic arch defined as a loss of luminal continuity between the ascending and descending portions of the aorta. In a simple interrupted aortic arch, only a ventricular septal defect and patent ductus arteriosus are observed. We present a rare complex form of type A interrupted aorta with an aortopulmonary window, an atrial septal ...