Pulmonary agenesis is a rare congenital anomaly in which there is absence of pulmonary parenchyma as well as its bold vessels. It is an unusual cause of respiratory distress in newborn. Unilateral agenesis of lung is often associated with other congenital anomalies. The condition may lead to diagnostic difficulties.   Right pulmonary agenesis has poor prognosis. Here we present a case of fem...

pulmonary agenesis is a very rare condition and many of them are associated with a variety of cardiac and non-cardiac malformations. we report an eight-month old girl with chronic lung infection due to right sided pulmonary agenesis without any associated major cardiac or non-cardiac abnormalities. the case brings in forth the importance of investigating any infant presenting with features of c...

unilateral pulmonary artery agenesis (upaa) is a rare congenital anomaly during the 4 th  week of gestational age. it is defined as an absence of pulmonary parenchyma and its supporting artery. a 9-year-old girl was admitted to our hospital because of chronic cough. chest examination showed a decrement in lung sound of right hemi-thorax with expiratory wheeze. chest radiography (cxr) revealed a...

one of the more infrequent congenital diseases with a wide spectrum of symptoms and more complications of the right side of pulmonary artery (63% according to ten harkel) is unilateral pulmonary artery agenesis (upaa). the clinical presentation is variable, and many patients can be asymptomatic for many years and even throughout their lives. although the disease more frequently appears in child...

UNLABELLED Unilateral pulmonary artery agenesis without any cardiovascular malformation is a rare anomaly. We present the imaging findings of a patient who was diagnosed as isolated left pulmonary artery agenesis. A 27-year-old female patient was admitted to our hospital due to dyspnea during exercise for five years. Chest X-ray revealed minimally small left pulmonary hilum and left lung. She w...

The combination of pulmonary agenesis and anophtalmia or microphthalmia has been described previously. This condition is known as Matthew-Wood syndrome and PDAC syndrome (pulmonary hypoplasia/ agenesis, diaphragmatic hernia/eventration, anophthalmia/microphthalmia, and cardiac defect). We report a sporadic case of female infant with the combination of bilateral microphthalmia, unilateral right ...

Pulmonary artery agenesis is one of several diagnostic possibilities which may present with similar chest roentgenographic features, including unilateral pulmonary hypoperfusion and nonvisualization of a pulmonary artery. We have applied ventilation and perfusion scintiphotography as an aid in differentiating agenesis from the other conditions with which it may be confused. Four patients presen...

Pulmonary agenesis is a rarely encountered congenital anomaly, and its average prevalence is about 1 in 100,000 births. Anomalies of the cardiovascular, musculoskeletal, gastrointestinal, or genitourinary systems may accompany in nearly half of the cases. The diagnosis of pulmonary agenesis is usually made during childhood, but the diagnosis may be delayed until adulthood in case of an absence ...

Left-sided pulmonary artery agenesis is a rare malformation that commonly requires childhood intervention secondary to associated congenital cardiovascular anomalies. We present an uncommon case of left-sided agenesis with an associated right-sided aortic arch and significant hypoplasia of the ipsilateral lung. Additionally, there is radiographic evidence of emphysema and pulmonary artery hyper...