Hereditary benign telangiectasia is an uncommon idiopathic skin disorder characterized by generalized telangiectases and angiomatous lesions of the skin. The diagnosis should be suspected in patients with such cutaneous lesions, positive family history, no associated bleeding problems, and no mucosal involvement. We present six cases of hereditary benign telangiectasia in three generations of o...

Hereditary haemorrhagic telangiectasia (HHT) is an autosomal, predominantly inherited disease characterized by diffuse telangiectases involving the skin, mucous membranes, lung, brain, gastrointestinal tract and liver. Peliosis hepatis is a rare, benign disorder causing sinusoidal dilatation and the presence of multiple blood-filled lacunar spaces within the liver. We report a case of an HHT pa...

Hereditary benign telangiectasia (HBT), first described in 1971,1 is a rare autosomal dominant disorder.2' 3, 4 It is characterised by widespread telangiectases which may be punctate, plaquelike, radiating or merely a diffuse blush. The lesions generally are observed before adolescence, and rarely during the first year of life.5 It is important to recognise HBT as it may only cause cosmetic dis...

conclusion the involved liver with hht typically shows vascular shunting and biliary diseases. also, arteriovenous shunts may be vulnerable to biliary diseases. results (i) three types of shunting were found in the livers, including arteriovenous (hepatic artery to hepatic vein) in 6 cases, arterioportal (hepatic artery to portal vein) in 2 cases, and portal venous (portal vein to hepatic vein)...

The properties of HBTs, HEMTs, PHEMTs and MESFETs are reviewed and discussed in the context of their suitability for various applications. Noise, power and high frequency performance is reviewed and the physical mechanisms dictating their values are discussed. The reliability characteristics of the devices are discussed and system applications are reported.

Dear Edito, A 60-year-old white female patient sought treatment for asymptomatic erythematous-telangiectasia macules on her upper limbs, back, abdomen, thighs, neck, and lips (Figures 1 and 2). The condition started at 7 years of age. Her lower limbs showed no skin alterations, and she never developed mucosal nor visceral bleeding. Darier’s sign was negative. She suffered from hypertension and ...

Hereditary hemorrhagic telangiectasia is an autosomal dominant disease in which arteriovenous communications are typically seen in the skin, mucosal surfaces, lungs, brain and gastrointestinal tract. This disease typically presents as epistaxis, gastrointestinal bleeding and arteriovenous malformations (in the brain and lungs). Although the epistaxis and gastrointestinal bleeding can result in ...