نتایج جستجو برای: triplication

تعداد نتایج: 451  

Journal: :Journal of Parkinson's disease 2011
Sally K Mak Deepika Tewari James W Tetrud J William Langston Birgitt Schüle

Mitochondrial dysfunction has been frequently implicated in the neurodegenerative process that underlies Parkinson's disease (PD), but the basis for this impairment is not fully understood. The goal of this study was to investigate the effects of α-synuclein (α-syn) gene multiplication on mitochondrial function in human tissue. To investigate this question, human fibroblasts were taken from a p...

Journal: :The Plant cell 2011
Andrew J Severin Steven B Cannon Michelle M Graham David Grant Randy C Shoemaker

With the advent of high-throughput sequencing, the availability of genomic sequence for comparative genomics is increasing exponentially. Numerous completed plant genome sequences enable characterization of patterns of the retention and evolution of genes within gene families due to multiple polyploidy events, gene loss and fractionation, and differential evolutionary pressures over time and ac...

2017
Hossein Jalali Mehrnoush Kosaryan Mohammad Reza Mahdavi Mehrad Mahdavi

Corresponding Author: Mohammad Reza Mahdavi Fajr Medical Laboratory, Keshavarz Blvd. Sari, Iran. Phone: +98-1133292929 E-mail: [email protected] Abstract Background: Alpha Thalassemia is one of the most prevalent disorders worldwide with a high carrier rate in Mazandaran province (north of Iran). Carriers of --MED double gene deletion are at risk of having a child with haemoglobin H (HbH)...

Journal: :Genetics 1993
T Freedman P J Pukkila

We have examined the stability of duplicated DNA sequences in the sexual phase of the life cycle of the basidiomycete fungus, Coprinus cinereus. We observed premeiotic de novo methylation in haploid nuclei containing either a triplication, a tandem duplication, or an ectopic duplication. Methylation changes were not observed in unique sequences. Repeated sequences underwent methylation changes ...

2017
Orna Steinberg-Shemer Jacob C. Ulirsch Sharon Noy-Lotan Tanya Krasnov Dina Attias Orly Dgany Ruth Laor Vijay G. Sankaran Hannah Tamary

Whole-exome sequencing (WES) has been increasingly useful for the diagnosis of patients with rare causes of anemia, particularly when there is an atypical clinical presentation or targeted genotyping approaches are inconclusive. Here, we describe a 20-yr-old man with a lifelong moderate-to-severe anemia with accompanying splenomegaly who lacked a definitive diagnosis. After a thorough clinical ...

Journal: :The Plant cell 2013
Shifeng Cheng Erik van den Bergh Peng Zeng Xiao Zhong Jiajia Xu Xin Liu Johannes Hofberger Suzanne de Bruijn Amey S Bhide Canan Kuelahoglu Chao Bian Jing Chen Guangyi Fan Kerstin Kaufmann Jocelyn C Hall Annette Becker Andrea Bräutigam Andreas P M Weber Chengcheng Shi Zhijun Zheng Wujiao Li Mingju Lv Yimin Tao Junyi Wang Hongfeng Zou Zhiwu Quan Julian M Hibberd Gengyun Zhang Xin-Guang Zhu Xun Xu M Eric Schranz

The Brassicaceae, including Arabidopsis thaliana and Brassica crops, is unmatched among plants in its wealth of genomic and functional molecular data and has long served as a model for understanding gene, genome, and trait evolution. However, genome information from a phylogenetic outgroup that is essential for inferring directionality of evolutionary change has been lacking. We therefore seque...

Journal: :Human molecular genetics 2013
Ariadna Laguna María-José Barallobre Miguel-Ángel Marchena Catarina Mateus Erika Ramírez Carmen Martínez-Cue Jean M Delabar Miguel Castelo-Branco Pedro de la Villa Maria L Arbonés

Down syndrome (DS) results from the triplication of approximately 300 human chromosome 21 (Hsa21) genes and affects almost all body organs. Children with DS have defects in visual processing that may have a negative impact on their daily life and cognitive development. However, there is little known about the genes and pathogenesis underlying these defects. Here, we show morphometric in vivo da...

2011
Annalisa Vetro Roberto Ciccone Roberto Giorda Maria Grazia Patricelli Erika Della Mina Antonella Forlino Orsetta Zuffardi

BACKGROUND SOX9 is a widely expressed transcription factor playing several relevant functions during development and essential for testes differentiation. It is considered to be the direct target gene of the protein encoded by SRY and its overexpression in an XX murine gonad can lead to male development in the absence of Sry. Recently, a family was reported with a 178 kb duplication in the gene...

Journal: :Brain : a journal of neurology 2004
Amanda Singleton Katrina Gwinn-Hardy Yehonotan Sharabi Sheng-Ting Li Courtney Holmes Raghuveer Dendi John Hardy Andrew Singleton Anthony Crawley David S Goldstein

Parkinson's disease patients frequently have symptoms and signs of autonomic nervous dysfunction that are the source of considerable disability. Recent studies have revealed that most patients with Parkinson's disease, and all with Parkinson's disease-associated orthostatic hypotension, have a loss of cardiac sympathetic innervation. Familial Parkinson's disease, caused by mutation of the gene ...

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