ataxia-telangiectasia (at) is an autosomal recessive disease characterized by telangiectasia, progressive ataxia, sinopulmonary infection, hypersensitivity to ionizing radiation, and a combined immunodeficiency, usually consisting of selective iga and igg, deficiencies, cutaneous anergy, and often depressed but not absent in vitro lymphocyte responsiveness. reviewing the medical records of 50 p...