Case presentation: Patient L.V.M.B., female, 3 months old, born and resident in Frutal-MG. She was admitted to the Pediatric Emergency Room of Hospital de Clínicas da UFTM, referred from city origin, due an unprecedented convulsive crisis 1 day ago, which characterized by spastic movements topography hemiface on right (right eye traction labial commissure) preceded hyporexia irritability, accor...

Incontinentia pigmenti is a rare X-linked genodermatosis that affects mainly female neonates. The first manifestation occurs in the early neonatal period and progresses through four stages: vesicular, verruciform, hyperpigmented and hypopigmented. Clinical features also manifest themselves through changes in the teeth, eyes, hair, central nervous system, bone structures, skeletal musculature an...

Incontinentia pigmenti is a rare X-linked genodermatosis that affects mainly female neonates. Skin manifestations are the most common and occur in four quite distinct phases. A female infant presented vesiculobullous lesions on trunk and limbs, and a verrucous lesion on the right palm. Biopsy revealed eosinophil exocytosis and pigment incontinence, confirming the clinical hypothesis. Although u...