نتایج جستجو برای: spastic paraplegia

تعداد نتایج: 11676  

Journal: :Annual Review of Neuroscience 2012

Journal: :Journal of Neurology, Neurosurgery & Psychiatry 1977

2017
Tian Li Li Tu Qian Zhang Ran Gu Qian Wang Bingjin Wang Huan Yao Xiang Qu Wenqin Wang Jinyong Tian

Objective: This study aimed to analyze the hereditary spastic paraplegia (HSP)/spastic paraplegia 3A (SpG3A) genomic structure as well as the polymorphisms in SPG3G genomic structure by comparing with the normal subjects. Methods: A total of 66 sporadic cases with HSP were collected from April 2014 to September 2016. Genomic DNA extraction was performed, and all coding exons and junction region...

Journal: :Orthopedics & Traumatology 1988

Journal: :Current Biology 2004
Robert M. Gould Scott T. Brady

Studies with animal models are providing new insights into the pathology of hereditary spastic paraplegia, particularly how mutations in multiple, converging pathways can lead to this family of neuropathies.

Journal: :Journal of medical genetics 2002
M Zortea A Vettori C P Trevisan S Bellini G Vazza M Armani A Simonati M L Mostacciuolo

It has been suggested that a genetic factor(s) or a familial predisposition may contribute to the clinical manifestations of disc herniation; moreover, no genetic linkage between spinal disc herniation and spastic paraplegia has ever been described. A family with consanguineous parents and four of eight sibs affected by multiple disc herniations and spastic paraplegia was clinically and genetic...

Journal: :Brain : a journal of neurology 2010
Christoph S Clemen Karthikeyan Tangavelou Karl-Heinz Strucksberg Steffen Just Linda Gaertner Hanna Regus-Leidig Maria Stumpf Jens Reimann Roland Coras Reginald O Morgan Maria-Pilar Fernandez Andreas Hofmann Stefan Müller Benedikt Schoser Franz-Georg Hanisch Wolfgang Rottbauer Ingmar Blümcke Stephan von Hörsten Ludwig Eichinger Rolf Schröder

Mutations of the human valosin-containing protein gene cause autosomal-dominant inclusion body myopathy associated with Paget disease of bone and frontotemporal dementia. We identified strumpellin as a novel valosin-containing protein binding partner. Strumpellin mutations have been shown to cause hereditary spastic paraplegia. We demonstrate that strumpellin is a ubiquitously expressed protein...

2016
Jennifer Hirst Marianna Madeo Katrien Smets James R. Edgar Ludger Schols Jun Li Anna Yarrow Tine Deconinck Jonathan Baets Elisabeth Van Aken Jan De Bleecker Manuel B. Datiles Ricardo H. Roda Joachim Liepert Stephan Züchner Caterina Mariotti Peter De Jonghe Craig Blackstone Michael C. Kruer

[This corrects the article on p. e98 in vol. 2, PMID: 27606357.].

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