We discuss the assessment and differential diagnoses of a young adult Hungarian man with a 1-year history of a progressive and symmetric amyotrophic lateral sclerosis-like syndrome, along with irregular action tremor and stimulus-sensitive myoclonus of the arms. MR scan of the brain showed isolated cerebellar atrophy and formal neuropsychometric testing identified significant subclinical defici...

We discuss the nonlinear extension to the integrated Sachs-Wolfe effect ~ISW! resulting from the divergence of the large scale structure momentum density field. The nonlinear ISW effect leads to an increase in the total ISW contribution by roughly two orders of magnitude at l;1000. This increase, however, is still below the cosmic variance limit of the primary anisotropies; at further small ang...

BACKGROUND The use of the extra-vertebral balloon osteoplasty is increasing and in the meanwhile it has become a safe surgical technique in the treatment of tibial head, distal radius and calcaneus fractures. In addition, we already could show in a biomechanical setup that the balloon osteoplasty might be a safe tool for reduction in the treatment of Hill-Sachs lesions, but clinical application...

Tay-Sachs disease is an autosomal recessive disorder affecting the central nervous system. The disorder results from mutations in the gene encoding the alpha-subunit of beta-hexosaminidase A, a lysosomal enzyme composed of alpha and beta polypeptides. Seventy-eight mutations in the Hex A gene have been described and include 65 single base substitutions, one large and 10 small deletions, and two...

A generalized dilaton action is considered of which the standard dilaton black hole and spherically reduced gravity are particular cases. The Arnowitt-Deser-Misner (ADM) and the Bondi-Sachs (BS) mass are calculated. Special attention is paid to both the asymptotic conditions for the metric as well as for the reference space-time. For the latter one we suggest a modified expression thereby obtai...

Following the recent recognition of a positive value for the vacuum energy density and the realization that a simple Kantowski-Sachs model might fit the classical tests of cosmology, we study the qualitative behavior of three anisotropic and homogeneous models: Kantowski-Sachs, Bianchi type-I and Bianchi type-III universes, with dust and a cosmological constant, in order to find out which are p...

BACKGROUND A Hill-Sachs lesion of the humeral head after a shoulder dislocation is clinically insignificant in most cases. However, a sizable defect will engage with the anterior rim of the glenoid and cause instability even after anterior glenoid reconstruction. The purpose of this study was to evaluate the outcome of arthroscopic capsulotenodesis of the posterior capsule and infraspinatus ten...

A cute traumatic posterior glenohumeral dislocations are rare; they are typically caused by high-velocity trauma, epileptic seizures, or electrocution. Anterior impression fractures of the humeral head (reverse Hill-Sachs defect) occur in over 80% of individuals following a posterior dislocation of the shoulder. The size of reverse Hill-Sachs defects varies and has been reported to be as large ...

Jeffrey Sachs is an economist so you may wonder whether this book contains information relevant for soil scientists. Well, it does! And let me tell you about this book, the author and why this book should be read by soil scientists fascinated by big questions, global issues and readable books. The book title refers John Maynard Keynes' from 1930 " Economic possibilities for our grandchildren "....

J effrey sachs is an economist, not an evangelist. But give the man 10 minutes behind a microphone, and a scholarly symposium starts to feel like a revival meeting. “Ladies and gentlemen,” he tells a hushed hall after describing how AIDS sufferers die in Malawi for want of $1-a-day drugs, “this plague is exploding. Its consequences will make the world quake. Rich countries could stop the devast...