A female infant with unilateral pulmonary agenesis developed congestive heart failure dominated by symptoms of obstructive disease of the airways at 3 1/2 months of age. Cardiac catheterization revealed total anomalous pulmonary venous connection to the right atrium. Despite a massive left-to-right shunt with one pulmonary artery receiving the entire right ventricular output since birth, the pa...

Four patients had pulmonary agenesis. All were symptomatic in infancy. In three, symptoms improved during two to six years of follow-up. One, who died at one month, had a unique combination of agenesis of the right upper and middle lobes and a hypoplastic right lower lobe supplied by systemic arteries from below the diaphragm, total anomalous pulmonary venous drainage to the left superior vena ...

Agenesis of the lung is not an uncommon anomaly, and when it is an isolated finding, it is compatible with even normal life (Hochberg & Naclerio 1955; Netterville 1957; Van Loon & Diamond 1962; Shenoy 1979). Hundreds of cases were reported in the world literature (Oyama et al. 1953; Valle 1955; Booth & Berry 1967; Maltz & Nadas 1968; Borja et al. 1970). Various associated malformations are comm...

Unilateral pulmonary artery agenesis (UPAA) is a rare congenital anomaly due to a malformation of the sixth aortic arch of the affected side during embryogenesis. It can occur in isolation or may be associated with other congenital cardiovascular malformations. The diagnosis is usually set at adolescence, however it can remain asymptomatic and late diagnosis is possible. Recurrent pulmonary inf...

A 55-year-old male with persistent atrial fibrillation (AF) and typical atrial flutter was admitted to our hospital for catheter ablation (CA). Enhanced computerized tomography (CT) before CA demonstrated a left shrunken lung and absence of the left main pulmonary artery (Panel A). Collateral flow via the coronary and bronchial arteries fed to the peripheral left pulmonary artery. All of the fo...