Mlle K.M, âgée de 19 ans, est suivie au service d'hématologie pour une LAL diagnostiqué sur les données cliniques (syndrome d'insuffisance médullaire, un syndrome tumoral important) et paracliniques (hyperleucocytose majeure à 145 720/mm3 et 95% de blastes). Le myélogramme et l'immunophénotypage confirmait le diagnostic de LAL biphénotypique T et B. Le caryotype était complexe. La patiente a ét...

OBJECTIVE Surgical repair of digital flexion deformities can result in vascular injuries threatening the viability of the affected digit. While uncommon, these injuries are reported to have a rate as high as 0.8% following palmo-digital fasciectomy for Dupuytren's disease. Late presentation of such vascular events pose a challenge, since taking the patient to the operating room does not guarant...

La maladie dermatophytique, décrite pour la première fois en 1959 par Hadida et Schousboe, est une infection dermatophytique chronique de la peau et des viscères. C'est une maladie rare principalement décrite au Maghreb. Les études immunologiques ont permis de mettre en évidence un déficit de l'immunité cellulaire à transmission autosomale récessive responsable d'un état de tolérance vis-à-vis ...

Les luxations et fractures péri-lunaires du carpe sont des traumatismes graves avec séquelles fonctionnelles fréquentes sévères. Notre objectif était d’évaluer les résultats cliniques radiographiques à long terme de ces lésions péri-lunaires, rechercher facteurs pronostiques mauvaise évolution clinique. Hypothèse Tous patients victimes présentent modifications radiologiques malgré une prise en ...

Background SAPHO is a heterogeneous autoinflammatory disease, characterized by bone and joint involvement wide variety of dermatologic manifestations, including palmo-plantar pustulosis (PPP), acne, hidradenitis suppurativa (HS), pyoderma gangrenosum (PG), psoriasis, Snedd-Wilkinson disease Sweet syndrome. In children, the osteo-articular manifestations are chronic recurrent multifocal osteomye...

A 36-year-old female offi ce clerk was admitted with a 6-week history of headache, abnormal behaviour (poor work performance, deteriorating table manners, and lack of social inhibition and frequent repetition of words or phrases) as well as unsteady gait. She also had episodes of urinary incontinence. On examination, she was found to be confused and disoriented. She had positive primitive refl ...

Lupi et al. present, on p. 80–81, an interesting case report of dyshidrosiform palmo-plantar pemphigoid. They describe a 20-year-old man who had had itchy vesicles on his palms and soles for 1 year. Histologically, a subepi-dermal vesicle was seen, and direct immunofluorescence showed continuous linear deposition of IgG and C 3 at the dermal-epidermal junction. An enzyme-linked immuno-sorbent a...

Triple A (AAA) syndrome (also known as Allgrove syndrome) is a rare multi systemic disorder. The disease usually manifests with adrenal insufficiency in early childhood. Apart from insufficiency, alacrima and achalasia represent the two other classical findings associated disease. Motor neuron like presentation of seldom reported literature. We describe case diagnosed since childhood who later ...

The antiphospholipid antibody syndrome is defined by the presence of antiphospholipid antibodies in patients with recurrent venous or arterial thromboembolism (1). SAPHO syndrome is a rare disease, characterized by specific clinical manifestations of synovitis, acne pustulosis, hyperostosis, and osteitis. It is a disease that manifests with a combination of osseous and articular manifestations ...