نتایج جستجو برای: monosomy 21

تعداد نتایج: 249214  

Journal: :Fertility and sterility 2015
Jorge Rodriguez-Purata Joseph Lee Michael Whitehouse Rose Marie Moschini Jaime Knopman Marlena Duke Benjamin Sandler Alan Copperman

OBJECTIVE To compare the incidence of numerical chromosomal abnormalities (NCAs) reported after preimplantation genetic screening (PGS) analysis compared with that reported after cytogenetic analysis of products of conception after spontaneous abortion. DESIGN Retrospective study. SETTING Private academic in vitro fertilization center. PATIENT(S) Cytogenetic reports of patients who underw...

2014
Pricila da Silva Cunha Heloisa B. Pena Carla Sustek D'Angelo Celia P. Koiffmann Jill A. Rosenfeld Lisa G. Shaffer Martin Stofanko Higgor Gonçalves-Dornelas Sérgio Danilo Junho Pena

Monosomy 1p36 is considered the most common subtelomeric deletion syndrome in humans and it accounts for 0.5-0.7% of all the cases of idiopathic intellectual disability. The molecular diagnosis is often made by microarray-based comparative genomic hybridization (aCGH), which has the drawback of being a high-cost technique. However, patients with classic monosomy 1p36 share some typical clinical...

Journal: :The British journal of ophthalmology 2004
M T Sandinha M A Farquharson F Roberts

BACKGROUND/AIMS In uveal melanoma monosomy 3 is emerging as a significant indicator of a poor prognosis. To date most cytogenetic studies of uveal melanoma have utilised fresh tissue or DNA extracted from tissue sections. In this study chromosome in situ hybridisation (CISH) was used to study monosomy 3 in tissue sections. The copy number of chromosome 3 was determined and related to patient su...

2016
Majd D. Jawad Ronald S. Go Rhett P. Ketterling Kebede H. Begna Kaaren K. Reichard Min Shi

Tyrosine kinase inhibitor treated chronic myelogenous leukemia patients with monosomy 7 arising in Philadelphia chromosome negative (Ph-) cells tend to evolve into MDS/AML. However, monosomy 7 in Ph- cells can be a transient finding, and it is not an absolute indication of the emergence of a new myeloid malignancy.

2013
Samin Alavi Maryam Ebadi Alireza Jenabzadeh M. T. Arzanian Sh. Shamsian

Herein, the first case of childhood erythrophagocytosis following chemotherapy for erythroleukemia in a child with monosomy 7 is reported. A 5-year-old boy presented with anemia, thrombocytopenia, and hepatosplenomegaly in whom erythroleukemia was diagnosed. Prolonged pancytopenia accompanied by persistent fever and huge splenomegaly and hepatomegaly became evident after 2 courses of chemothera...

2018
Victor B. Pastor Sushree S. Sahoo Jessica Boklan Georg C. Schwabe Ebru Saribeyoglu Brigitte Strahm Dirk Lebrecht Matthias Voss Yenan T. Bryceson Miriam Erlacher Gerhard Ehninger Marena Niewisch Brigitte Schlegelberger Irith Baumann John C. Achermann Akiko Shimamura Jochen Hochrein Ulf Tedgård Lars Nilsson Henrik Hasle Melanie Boerries Hauke Busch Charlotte M. Niemeyer Marcin W. Wlodarski

Familial myelodysplastic syndromes arise from haploinsufficiency of genes involved in hematopoiesis and are primarily associated with early-onset disease. Here we describe a familial syndrome in seven patients from four unrelated pedigrees presenting with myelodysplastic syndrome and loss of chromosome 7/7q. Their median age at diagnosis was 2.1 years (range, 1-42). All patients presented with ...

Journal: :Journal of medical genetics 1999
R Valero G Marfany R Gil-Benso M A Ibáñez I López-Pajares F Prieto G Rullan E Sarret R Gonzàlez-Duarte

Although trisomy of chromosome 21 is the most prevalent human genetic disorder, data from partial 21 aneuploidies are very scanty. Eight different partial aneuploidies for chromosome 21 were characterised by fluorescence quantitative PCR. Allelic dosage analysis was performed for each patient using 25 CHLC STRs covering the entire q arm. The length of the corresponding trisomies and monosomies ...

Journal: :Blood 2016
Marcin W Wlodarski Shinsuke Hirabayashi Victor Pastor Jan Starý Henrik Hasle Riccardo Masetti Michael Dworzak Markus Schmugge Marry van den Heuvel-Eibrink Marek Ussowicz Barbara De Moerloose Albert Catala Owen P Smith Petr Sedlacek Arjan C Lankester Marco Zecca Victoria Bordon Susanne Matthes-Martin Jonas Abrahamsson Jörn Sven Kühl Karl-Walter Sykora Michael H Albert Bartlomiej Przychodzien Jaroslaw P Maciejewski Stephan Schwarz Gudrun Göhring Brigitte Schlegelberger Annámaria Cseh Peter Noellke Ayami Yoshimi Franco Locatelli Irith Baumann Brigitte Strahm Charlotte M Niemeyer

Germline GATA2 mutations cause cellular deficiencies with high propensity for myeloid disease. We investigated 426 children and adolescents with primary myelodysplastic syndrome (MDS) and 82 cases with secondary MDS enrolled in 2 consecutive prospective studies of the European Working Group of MDS in Childhood (EWOG-MDS) conducted in Germany over a period of 15 years. Germline GATA2 mutations a...

نمودار تعداد نتایج جستجو در هر سال

با کلیک روی نمودار نتایج را به سال انتشار فیلتر کنید