The surgical armamentarium for the treatment of massive facial trauma has undergone a dramatic shift from early management strategies. Although tenants acute continue to prioritize airway and cardiopulmonary support, improved functional outcomes are achievable with an emphasis on definitive free tissue transfer. use workhorse donor flaps, such as radial forearm, fibula, latissimus, have become ...

Freeman-Sheldon syndrome (FSS) is a rare form of multiple congenital contracture syndrome and is the most severe form of distal arthrogryposis. Described in 1938 by Freeman and Sheldon, it is also referred to as distal arthrogryposis type 2A, craniocarpotarsal dysplasia or whistling faceewindmill vane hand syndrome. Its main form of inheritance is autosomal dominant, but it can also be autosoma...

OBJECTIVE A case of extreme microstomia in an 8-month-old infant is presented. As a result of caustic acid ingestion at the age of a few weeks, the male infant developed progressive stricture of the perioral region preventing him from normal food intake. METHODS The patient was treated by bilateral commissurotomies and a total of 4 rhomboid flaps based in the buccal mucosa. RESULTS We were ...

Epidermolysis bullosa (EB) is a heterogeneous group of rare genetic disorders characterized by marked fragility of the skin and mucous membranes in which vesiculobullous lesions occur in response to trauma, heat or no apparent cause. The recessive form of EB presents the greatest oral alterations including repeated blistering and scar formation leading to limited oral opening, ankyloglossia, to...