نتایج جستجو برای: leigh syndrome

تعداد نتایج: 623686  

Journal: :Journal of Institute of Medicine Nepal 2020

2004
Richard N. Mitchell Andrew H. Lichtman

1. DiMauro, S., and Schon, E.A. 2003. Mitochondrial respiratory-chain diseases. N. Engl. J. Med. 348:2656–2668. 2. Janssen, R.J., Van Den Heuvel, L.P., and Smeitink, J.A. 2004. Genetic defects in the oxidative phosphorylation (OXPHOS) system. Expert Rev. Mol. Diagn. 4:143–156. 3. Zhu, Z., et al. 1998. SURF1, encoding a factor involved in the biogenesis of cytochrome c oxidase, is mutated in Lei...

2014
Chiara La Morgia Leonardo Caporali Francesca Gandini Anna Olivieri Francesco Toni Stefania Nassetti Daniela Brunetto Carlotta Stipa Cristina Scaduto Antonia Parmeggiani Caterina Tonon Raffaele Lodi Antonio Torroni Valerio Carelli

BACKGROUND An increasing number of mitochondrial DNA (mtDNA) mutations, mainly in complex I genes, have been associated with variably overlapping phenotypes of Leber's hereditary optic neuropathy (LHON), mitochondrial encephalomyopathy with stroke-like episodes (MELAS) and Leigh syndrome (LS). We here describe the first case in which the m.4171C>A/MT-ND1 mutation, previously reported only in as...

Journal: :Molecular Genetics and Metabolism Reports 2018

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