نتایج جستجو برای: hyper igm

تعداد نتایج: 40595  

Journal: :Journal of immunology 1999
S Lacroix-Desmazes I Resnick D Stahl L Mouthon T Espanol J Levy S V Kaveri L Notarangelo M Eibl A Fischer H Ochs M D Kazatchkine

We have analyzed the self-reactive repertoires of IgM and IgG Abs in the serum of 19 patients with hyper-IgM syndrome (HIM) by means of a quantitative immunoblotting technique that allows for a quantitative comparison of Ab repertoires in health and disease by multiparametric statistical analysis. Normal tissue extracts of liver, lung, stomach, and kidney were used as sources of self Ags. Extra...

2012
Silvia Montella Marco Maglione Giuliana Giardino Angela Di Giorgio Loredana Palamaro Virginia Mirra Matilde Valeria Ursini Mariacarolina Salerno Claudio Pignata Carlo Caffarelli Francesca Santamaria

The Hyper-immunoglobulin M syndromes (HIGM) are a heterogeneous group of genetic disorders resulting in defects of immunoglobulin class switch recombination. Affected patients show humoral immunodeficiency and high susceptibility to opportunistic infections. Elevated serum IgM levels are the hallmark of the disease, even though in few rare cases they may be in the normal range. Hyper IgM is ass...

Journal: :The Malaysian journal of pathology 1992
L M Noh S M Low I Lajin N Abdullah

A 20-month-old Indian boy presented with recurrent pyogenic infections and failure to thrive. His IgG and IgA levels were low, but his IgM was elevated. He also had undetectable isohaemagglutinin titre and neutropenia, both parameters being poor prognostic indicators in this very rare primary immunodeficiency state--antibody deficiency with hyper IgM. Our patient subsequently succumbed to Pseud...

Journal: :Chang Gung medical journal 2003
Chun-Fong Huang Chih-Lu Wang Yung-Feng Huang Kai-Sheng Hsieh Kuender D Yang

Hyper-IgM syndrome (HIM) is a rare disorder resulting from mutation in the CD40 ligand (CD40L) gene. This defect is associated with normal or elevated serum level of IgM and with low to undetectable levels of serum IgG, IgA, IgE. This case of HIM with CD40L deficiency was proven by flow cytometry but initially presented as interstitial pneumonia. Pneumocystis carinii pneumonia was highly sugges...

Journal: :Biochimica et Biophysica Acta (BBA) - Molecular Basis of Disease 2006

نمودار تعداد نتایج جستجو در هر سال

با کلیک روی نمودار نتایج را به سال انتشار فیلتر کنید