نتایج جستجو برای: hyper ige syndrome

تعداد نتایج: 654501  

Journal: :Japanese Journal of Clinical Immunology 2010

2010
Sean A. McGhee Talal A. Chatila

DOCK8 deficiency is a newly described primary immune deficiency resulting in profound susceptibility to cutaneous viral infections, elevated IgE levels, and eosinophilia, but lacking in the skeletal manifestations commonly seen in hyper IgE syndrome, which it otherwise resembles. Although little is known about the DOCK8 protein, it resembles other atypical guanine exchange factors in the DOCK f...

Journal: :The Journal of clinical investigation 1994
M E Conley M Larché V R Bonagura A R Lawton R H Buckley S M Fu E Coustan-Smith H G Herrod D Campana

Recent studies show that most patients with X-linked hyper IgM syndrome have defects in the gene for CD40 ligand. We evaluated 17 unrelated males suspected of having X-linked hyper IgM syndrome. Activated T cells from 13 of the 17 patients failed to bind a soluble CD40 construct. In these patients, the sequence of CD40 ligand demonstrated mutations. By contrast, T cells from the remaining four ...

Journal: :Pediatric Hematology/Oncology and Immunopathology 2019

Journal: :European Annals of Allergy and Clinical Immunology 2017

Journal: :The Journal of clinical investigation 1981
R S Geha E Reinherz D Leung K T McKee S Schlossman F S Rosen

The status of suppressor T cells (Ts) was assessed in seven children with the hyper IgE syndrome (recurrent staphylococcal infections, eczematous skin rash, and elevated serum IgE) to determine whether a deficiency in Ts is associated with increased IgE synthesis. When circulating T cells and their subsets were enumerated with the aid of monoclonal antibodies that identify T cells (T3), helper/...

نمودار تعداد نتایج جستجو در هر سال

با کلیک روی نمودار نتایج را به سال انتشار فیلتر کنید