نتایج جستجو برای: ewing

تعداد نتایج: 2735  

2014
Allison F. O'Neill Jason L.J. Dearling Yuchuan Wang Tanya Tupper Yanping Sun Jon C. Aster Monica L. Calicchio Antonio R. Perez-Atayde Alan B. Packard Andrew L. Kung

Purpose: Ewing sarcoma is a tumor of the bone and soft tissue characterized by diffuse cell membrane expression of CD99 (MIC2). Single-site, surgically resectable disease is associated with an excellent 5-year event-free survival; conversely, patientswith distantmetastases have a poor prognosis.Noninvasive imaging is the standard approach to identifying sites of metastatic disease. We sought to...

2013
William Phillips Mary M Torchia

An overview of the presentation, clinical and radiographic features, and management of the most common benign pediatric bone tumors will be presented below. Malignant bone tumors (Ewing sarcoma and osteosarcoma) are discussed separately. (See "Clinical presentation, staging, and prognostic factors of the Ewing sarcoma family of tumors" and "Osteosarcoma: Epidemiology, pathogenesis, clinical pre...

2015
Monica Malik Irukulla Deepa M Joseph

Introduction: Ewing sarcoma family of tumors (ESFT) are a group of small round cell tumors showing varying degrees of neuroectodermal differentiation with Ewing sarcoma being the least differentiated. Primitive neuroectodermal tumors (PNET) show neuroectodermal differentiation by light microscopy, immune histochemistry (IHC) or electron microscopy [1]. According to WHO classification of bone an...

Journal: :international journal of hematology-oncology and stem cell research 0
kourosh goudarzi pour pediatric congenital hematologic disorders research center, shahid beheshti university of medical sciences, tehran, iran samin alavi pediatric congenital hematologic disorders research center, shahid beheshti university of medical sciences, tehran, iran shahin shamsian pediatric congenital hematologic disorders research center, shahid beheshti university of medical sciences, tehran, iran roxana aghakhani pediatric congenital hematologic disorders research center, shahid beheshti university of medical sciences, tehran, iran mohammad taghi arzanian pediatric congenital hematologic disorders research center, shahid beheshti university of medical sciences, tehran, iran hesameddin hoseini tavassol pediatric congenital hematologic disorders research center, shahid beheshti university of medical sciences, tehran, iran

treatment with intensification of chemotherapy using alkylating agents and topoisomerase ii inhibitors and radiotherapy has improved the outcome of patients with solid tumors such as ewing’s sarcoma. however, there are several reports of secondary malignancy following treatment of these tumors. in this article, we describe a 12 years old girl with all who had ewing’s sarcoma when she was 8 year...

Journal: :The Journal of clinical investigation 2014
Michelle Marques Howarth David Simpson Siu P Ngok Bethsaida Nieves Ron Chen Zurab Siprashvili Dedeepya Vaka Marcus R Breese Brian D Crompton Gabriela Alexe Doug S Hawkins Damon Jacobson Alayne L Brunner Robert West Jaume Mora Kimberly Stegmaier Paul Khavari E Alejandro Sweet-Cordero

Chromosomal translocation that results in fusion of the genes encoding RNA-binding protein EWS and transcription factor FLI1 (EWS-FLI1) is pathognomonic for Ewing sarcoma. EWS-FLI1 alters gene expression through mechanisms that are not completely understood. We performed RNA sequencing (RNAseq) analysis on primary pediatric human mesenchymal progenitor cells (pMPCs) expressing EWS-FLI1 in order...

Journal: :Cancer research 2014
Jozef Ban Dave N T Aryee Argyro Fourtouna Wietske van der Ent Max Kauer Stephan Niedan Isidro Machado Carlos Rodriguez-Galindo Oscar M Tirado Raphaela Schwentner Piero Picci Adrienne M Flanagan Verena Berg Sandra J Strauss Katia Scotlandi Elizabeth R Lawlor Ewa Snaar-Jagalska Antonio Llombart-Bosch Heinrich Kovar

The developmental receptor NOTCH plays an important role in various human cancers as a consequence of oncogenic mutations. Here we describe a novel mechanism of NOTCH-induced tumor suppression involving modulation of the deacetylase SIRT1, providing a rationale for the use of SIRT1 inhibitors to treat cancers where this mechanism is inactivated because of SIRT1 overexpression. In Ewing sarcoma ...

Journal: :Clinical cancer research : an official journal of the American Association for Cancer Research 2016
Christy L Osgood Nichole Maloney Christopher G Kidd Susan Kitchen-Goosen Laura Segars Meti Gebregiorgis Girma M Woldemichael Min He Savita Sankar Stephen L Lessnick Min Kang Malcolm Smith Lisa Turner Zachary B Madaj Mary E Winn Luz-Elena Núñez Javier González-Sabín Lee J Helman Francisco Morís Patrick J Grohar

PURPOSE The goal of this study was to identify second-generation mithramycin analogues that better target the EWS-FLI1 transcription factor for Ewing sarcoma. We previously established mithramycin as an EWS-FLI1 inhibitor, but the compound's toxicity prevented its use at effective concentrations in patients. EXPERIMENTAL DESIGN We screened a panel of mithralogs to establish their ability to i...

2016
Peter M. Anderson Stefan S. Bielack Richard G. Gorlick Keith Skubitz Najat C. Daw Cynthia E. Herzog Odd R. Monge Alvaro Lassaletta Erica Boldrini Zsuzanna Pápai Joseph Rubino Kumudu Pathiraja Darcy A. Hille Mark Ayers Siu‐Long Yao Michael Nebozhyn Brian Lu David Mauro

BACKGROUND Robatumumab (19D12; MK-7454 otherwise known as SCH717454) is a fully human antibody that binds to and inhibits insulin-like growth factor receptor-1 (IGF-1R). This multiinstitutional study (P04720) determined the safety and clinical efficacy of robatumumab in three separate patient groups with resectable osteosarcoma metastases (Group 1), unresectable osteosarcoma metastases (Group 2...

2014
Britta Vormoor Henrike K. Knizia Michael A. Batey Gilberto S. Almeida Ian Wilson Petra Dildey Abhishek Sharma Helen Blair I. Geoff Hide Olaf Heidenreich Josef Vormoor Ross J. Maxwell Chris M. Bacon

Ewing sarcoma and osteosarcoma represent the two most common primary bone tumours in childhood and adolescence, with bone metastases being the most adverse prognostic factor. In prostate cancer, osseous metastasis poses a major clinical challenge. We developed a preclinical orthotopic model of Ewing sarcoma, reflecting the biology of the tumour-bone interactions in human disease and allowing in...

Introduction: Ewing sarcoma (ES), which is described as diffuse endothelioma of the bone, is divided into osseous and extraosseous Ewing sarcoma (EES) mostly affecting children and adolescents. It is a rare, aggressive, and poorly differentiated small blue round cell tumor that seldom affects the head and neck regions.   Case Report: Herein, we reported a 46-year-old ma...

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