Budd-Chiari Syndrome is an uncommon condition characterized by clinical features related to hepatic venous outflow obstruction resulting either from thrombotic or non-thrombotic causes. Presentations may vary asymptomatic acute fulminant failure. A meticulous history, examination and imaging studies are invaluable for a prompt diagnosis initiation of time-sensitive treatment. This report presen...

A case of Budd-Chiari syndrome in a young woman, which started probably in the last trimester of pregnancy, is described. The diagnosis was made clinically and was confirmed by inferior venacavography and on exploratory laparotomy. The possible connection of the syndrome with the pregnancy is discussed.

A 27-years old female patient presented with a severe general condition of generalized edema and hypotension. Two months earlier computed tomography imaged thrombosis the inferior vena cava three hepatic veins, or Budd-Chiari syndrome (BCS). Additional findings were right common iliac vein renal veins bilaterally. Genetic testing proved congenital thrombophilia. Anticoagulation therapy did not ...

Budd Chiari syndrome or hepatic venous outflow obstruction is a complex entity with multiple etiologies and various clinical manifestations. It is often difficult to establish the diagnosis. The most common cause is a hypercoagulable state due to either genetic disorders of blood coagulation or several acquired conditions such as hematological diseases, tumors, infections, chronic inflammatory ...

Paroxysmal nocturnal hemoglobinuria (PNH) is associated with severe end-organ damage and a high risk of thrombosis. Budd-Chiari syndrome, which develops after thrombotic occlusion of major hepatic blood vessels, is relatively common in PNH and has been associated with increased mortality. We report the case of a 46-year-old male with PNH who presented with Budd-Chiari syndrome associated with p...