Budd Chiari syndrome or hepatic venous outflow obstruction is a complex entity with multiple etiologies and various clinical manifestations. It is often difficult to establish the diagnosis. The most common cause is a hypercoagulable state due to either genetic disorders of blood coagulation or several acquired conditions such as hematological diseases, tumors, infections, chronic inflammatory ...

Paroxysmal nocturnal hemoglobinuria (PNH) is associated with severe end-organ damage and a high risk of thrombosis. Budd-Chiari syndrome, which develops after thrombotic occlusion of major hepatic blood vessels, is relatively common in PNH and has been associated with increased mortality. We report the case of a 46-year-old male with PNH who presented with Budd-Chiari syndrome associated with p...

INTRODUCTION Scimitar syndrome is a congenital heart disease characterized by an abnormal drainage of the right lung into the inferior vena cava, the right atrium or a variety of venous connections from the anomalous pulmonary vein to a systemic vein. This left-to-right shunt induces pulmonary hypertension and is an indication for surgical repair in cases of a history of recurrent pneumonia or ...

A 34-year-old woman with primary antiphospholipid syndrome was admitted to the Gastroenterology Department of our hospital with fever, acute abdomen, watery diarrhea, and extremely high levels of inflammatory parameters. She had a history of left lower limb deep vein thrombosis and pulmonary embolism and was taking warfarin potassium. Acute gastroenteritis was suspected and an antibiotic was ad...

BACKGROUND The operations with proven effects on survival in Budd-Chiari syndrome are shunt operations and liver transplantation. PATIENTS AND METHODS Between 1993 and 1999 (June), 13 cases of Budd-Chiari syndrome have been treated surgically. Four cases had concomitant thrombosis of the inferior vena cava; the others had marked narrowing of the lumen due to the enlarged caudate lobe. Mesoatr...

Budd-Chiari Syndrome is an uncommon condition characterized by clinical features related to hepatic venous outflow obstruction resulting either from thrombotic or non-thrombotic causes. Presentations may vary asymptomatic acute fulminant failure. A meticulous history, examination and imaging studies are invaluable for a prompt diagnosis initiation of time-sensitive treatment. This report presen...

The histopathological changes in Budd–Chiari syndrome (BCS) overlap with those of sinusoidal obstruction (SOS) and cardiac or pericardiac disorders resulting right failure. These conditions, however, are different on both clinical pathological grounds need to be differentiated from BCS. This review is centred the three main aspects BCS diagnostic liver histopathology: (1) general histopathology...