Materials and methods 20 children (median age 10.6 years (1–16.6); 10 males) with PSV at various stages of disease activity were studied. PSV was classified as: polyarteritis nodosa (n = 10); Wegener's granulomatosis (n = 6); Kawasaki disease (n = 2); Behçet's disease (n = 1) and unclassified (n = 1). EPCs were detected using flow cytometry and defined as cells triple-positive for CD34, CD133, ...