نتایج جستجو برای: aldrich syndrome

تعداد نتایج: 623385  

Journal: :Indian Journal of Trauma and Emergency Pediatrics 2020

1998
A. Petrella I. Doti V. Agosti P. Carandente Giarrusso D. Vitale H. M. Bond C. Cuomo P. Tassone B. Franco A. Ballabio S. Venuta G. Morrone

Journal: :International immunology 2003
Vadim I Pivniouk Scott B Snapper Alexander Kettner Harri Alenius Dhafer Laouini Hervé Falet John Hartwig Frederick W Alt Raif S Geha

Wiskott-Aldrich syndrome protein (WASP) is the product of the gene deficient in boys with X-linked Wiskott-Aldrich syndrome. We assessed the role of WASP in signaling through the high-affinity IgE receptor (FcepsilonRI) using WASP-deficient mice. IgE-dependent degranulation and cytokine secretion were markedly diminished in bone marrow-derived mast cells from WASP-deficient mice. Upstream signa...

2014
Mitsuru Sato Katsura Kojima Chisato Sakuma Maria Murakami Yasushi Tamada Hiroshi Kitani

Bombyx mori (silkworm) silk proteins have been utilized as unique biomaterials for various medical applications. To develop a novel affinity silk material, we generated a transgenic silkworm that spins silk protein containing the fibroin L-chain linked with the single-chain variable fragment (scFv) as a fusion protein. Previously, the scFv-conjugated "affinity" silk powder specifically immunopr...

Journal: :Proceedings of the National Academy of Sciences of the United States of America 2003
Jordan S Orange K Eliza Harris Milena M Andzelm Markus M Valter Raif S Geha Jack L Strominger

Natural killer (NK) cells form a structure at their interface with a susceptible target cell called the activating NK cell immunologic synapse (NKIS). The mature activating NKIS contains a central and peripheral supramolecular activation cluster (SMAC), and includes polarized surface receptors, filamentous actin (F-actin) and perforin. Evaluation of the NKIS in human NK cells revealed CD2, CD11...

Journal: :Proceedings of the National Academy of Sciences of the United States of America 1999
S Linder D Nelson M Weiss M Aepfelbacher

Wiskott-Aldrich syndrome protein (WASp) is a hematopoietic-specific, multidomain protein whose mutation is responsible for the immunodeficiency disorder Wiskott-Aldrich syndrome. WASp contains a binding motif for the Rho GTPase CDC42Hs as well as verprolin/cofilin-like actin-regulatory domains, but no specific actin structure regulated by CDC42Hs-WASp has been identified. We found that WASp col...

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