Harlequin ichthyosis is a very rare condition that affects the skin of newborns. It is associated with poor barrier function of the skin leading to dehydration and leaves newborns prone to infections. It is due to mutations in adenosine triphosphate binding cassette A12 gene transmitted as an autosomal recessive disorder. The prognosis is very poor in these cases. Here, we report one such rare ...

and a 5% level of significance, seven different associations appear to be valid. However, when the p value is corrected by multiplying it by the number of factors investigated, only the association of HL-A12 with lymphocytic lymphomas and the 4c antigen with chronic lymphatic leukemia appear to be significant. The previously described increased incidence of W5 and 4c in Hodgkin's disease was no...

A12-month-old child was evaluated for pulmonary atresia with ventricular septal defect. Assessment of the whole arterial pulmonary arborization was first done by angiography. This examination revealed that the left lung received vascularization by the native pulmonary artery via a central shunt performed during the neonatal period and by 2 aortopulmonary collateral arteries. The positions of th...

Stephen J. Martin, Nicolas Châline, Benjamin P. Oldroyd, Graeme R. Jones, and Francis L. W. Ratnieks Laboratory of Apiculture and Social Insects, Department of Animal and Plant Sciences, University of Sheffield, Western Bank, Sheffield, S10 2TN, United Kingdom, School of Biological Sciences A12, University of Sydney, Sydney, New South Wales 2006, Australia, and Chemical Ecology Group, School of...

Our research is a variant of the third party punishment game. In particular, we want to test whether players have heterogeneous preferences; the levels of the sanction and of the transfer are proportional to the unfairness of the Dictator; the change of the role influences the Observer’s reaction to unfair behavior; players’ decision to punish the Dictator and/or to help the Receiver depends on...

triple a syndrome (allgrove syndrome) is a rare inherited autosomal recessive disease with a typical triad including adrenocorticotrophic-hormone-resistant glucocorticoid insufficiency, reduced or absent tearing (alacrima) and achalasia and a wide range of symptoms can be detected due to multi organ involvement. this report describes the case of a triple asyndrome, a12 year-old boy with a histo...

This articles investigates the recent trends in co-authorship in economics. Using data from more than 700.000 journal articles we show that the average number of authors per has increased over the last years. This process is likely to be continued in the future. In a regression analysis we present evidence how the authorship of papers is related to the number of citations, the JEL classificatio...

This paper deals with hyperbolic discounting in a macro context. Time consistency is discussed in terms of rational behavior and rational expectations. The theory is applied to the intertemporal consumption decision in order to explain undersaving in an economy. Moreover, possible implications on policy makers’ decisions on reforms and budget deficits are evinced. Finally, the Ricardian equival...

Jamal and Sunder (1996) showed that the median prices in double auctions populated by zero-intelligence (ZI) traders whose trading limits are set by two biased heuristics tend to converge to the same equilibrium as if their trading limits were set by applying Bayes’ Rule. This note provides an analytical explanation of why the repeated use of biased heuristics approximates Bayes rule. JEL class...