نتایج جستجو برای: thyroid dysgenesis

تعداد نتایج: 85068  

Journal: :Journal of medical genetics 1971
P L Townes W L Bradford

This report describes monozygous twin girls with different forms of thyroid dysfunction. Twin A was found to have athyreotic hypothyroidism during the first week of life; twin B developed acute hyperthyroidism at 16 years of age. While concordance and discordance for congenital hypothyroidism has been reported in several sets of twins (Table I) there have been no prior reports of congenital hyp...

2016
Shiguo Liu Jian Chai Guohua Zheng Huichao Li Deguo Lu Yinlin Ge

OBJECTIVE Congenital hypothyroidism (CH) is a frequent neonatal endocrine disease with an incidence of about 1:2500 worldwide. Although thyroid dysgenesis (TD) is the most frequent cause of CH cases, its pathogenesis remains unclear. The aim of this study was to screen the hematopoietically-expressedhomeobox gene (HHEX) mutations in Chinese children with TD. METHODS Genomic deoxyribonucleic a...

Journal: :The Journal of Clinical Endocrinology & Metabolism 2002

Amirhossein Tamimi, Atena Tamimi, Fatemeh Rajaeipoor, Manijeh Tabrizi, Marjaneh Zarkesh, Setila Dalili, Seyyedeh Azadeh Hoseini Nouri, Shahin Koohmanaee, Soroush Ahmadimacciani, Vahid Aminzadeh,

Background: Gonadal dysgenesis, the most common cause of primary amenorrhea, is characterized by absent or underdeveloped ovaries. Although the coexistence of gonadal dysgenesis and Mayer-Rokitansky-Küster-Hauser (MRKH) has been reported, it is still quite infrequent. To the extent that authors searched, just one study reported the association between Rokitansky sequence and Dandy-Walker malfor...

Journal: :Archives of endocrinology and metabolism 2015
Taise Lima de Oliveira Cerqueira Yanne Ramos Giorgia Strappa Daniel San Martin Mariana Jesus Jailciele Gonzaga Paulo Ferreira Anabel Costa Vladimir Fernandes Tatiana Amorim Ana Marice Ladeia Helton Ramos

OBJECTIVE To search for genetic alteration in NKX2.5 gene in patients presenting both congenital heart disease (CHD) and TD. SUBJECTS AND METHODS Individual phenotypes were carefully analyzed in 86 children with thyroid dysgenesis (TD) using thyroid function tests, scintigraphy, ultrasound and echocardiography. DNA was extracted and NKX2.5 gene coding region was amplified by polymerase chain ...

2015
Fabien Magne Roman Serpa Guy Van Vliet Mark E. Samuels Johnny Deladoëy

BACKGROUND/AIMS Congenital primary hypothyroidism (CH) is a rare pediatric disorder estimated to occur in about 1:2,500 live births. Approximately half of these cases entail ectopic thyroid tissue, which is believed to result from a migration defect during embryogenesis. Approximately 3% of CH cases are explained by mutation(s) in known genes, most of which are transcription factors implicated ...

Journal: :Pediatrics 2010
John S Parks Michelle Lin Scott D Grosse Cynthia F Hinton Margaret Drummond-Borg Lynette Borgfeld Kevin M Sullivan

The reported incidence rate of primary congenital hypothyroidism (CH) has been increasing in the United States over the past 2 decades. We have considered the possibility that the inclusion of cases of transient hypothyroidism has inflated the reported incidence rate of CH. Assessing the effects of cases of transient hypothyroidism on the incidence rate is problematic, because the definitions, ...

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