Congenital complete AV block (CAVB) affects 1 in 20 000 live-born infants2 and is commonly associated with an immune-related cause associated with maternal collagen vascular disease or structural cardiac disease.3 Other causes of CAVB have been described, including infections, myopathies, and genetic disorders such as the Hunter and Hurler syndromes. Still, the specific cause of CAVB remains el...