نتایج جستجو برای: six1

تعداد نتایج: 387  

Journal: :American journal of medical genetics. Part A 2008
Zhishuo Ou Donna M Martin Jirair K Bedoyan M Lance Cooper A Craig Chinault Pawel Stankiewicz Sau W Cheung

We report on a 26-month-old boy with developmental delay and multiple congenital anomalies, including many features suggestive of either branchiootorenal syndrome (BOR) or oculoauriculovertebral spectrum (OAVS). Chromosomal microarray analysis (CMA) initially revealed a copy-number gain with a single BAC clone (RP11-79M1) mapping to 14q23.1. FISH analysis showed that the third copy of this geno...

2013
Adriana Eisner Rosalind Segal

The Hedgehog (Hh) signaling pathway is vital for vertebrate embryogenesis and aberrant activation of the pathway can cause tumorigenesis in humans. In this study, we used a phosphatome RNAi screen for regulators of Hh signaling to identify a member of the Eyes Absent protein family, Eya1, as a positive regulator of Hh signal transduction. Eya1 is both a phosphatase and transcriptional regulator...

Journal: :European review for medical and pharmacological sciences 2014
G-W Feng L-D Dong W-J Shang X-L Pang J-F Li L Liu Y Wang

OBJECTIVES Histone deacetylases (HDACs) plays important roles in the regulation of genes expression and contribute to the growth of cancer cells. The present study aimed to investigate the function of HDAC5 in human hepatocellular carcinoma (HCC). PATIENTS AND METHODS The expression of HDAC5 in human hepatocellular carcinoma tissues and cells was detected. MTT assay was used to measure the pr...

Journal: :Development 2017
Andre L P Tavares Timothy C Cox Robert M Maxson Heide L Ford David E Clouthier

Jaw morphogenesis is a complex event mediated by inductive signals that establish and maintain the distinct developmental domains required for formation of hinged jaws, the defining feature of gnathostomes. The mandibular portion of pharyngeal arch 1 is patterned dorsally by Jagged-Notch signaling and ventrally by endothelin receptor A (EDNRA) signaling. Loss of EDNRA signaling disrupts normal ...

Journal: :American journal of clinical pathology 2014
Daniel Sehic Cristina D Ciornei David Gisselsson

OBJECTIVES Successful further treatment of Wilms tumors (WTs) after preoperative chemotherapy and surgery depends on correct histopathologic risk stratification, including quantification of remaining blastemal elements. In the present study, we assessed the usefulness of protein markers for the detection of WT blastema. METHODS Expression of the candidate blastemal protein markers CITED1, SIX...

2017
Roméo Sébastien Blanc Gillian Vogel Xing Li Zhenbao Yu Shawn Li Stéphane Richard

Quiescent muscle stem cells (MSCs) become activated in response to skeletal muscle injury to initiate regeneration. Activated MSCs proliferate and differentiate to repair damaged fibers or self-renew to maintain the pool and ensure future regeneration. The balance between self-renewal, proliferation, and differentiation is a tightly regulated process controlled by a genetic cascade involving de...

2018
Herui Wang Chi Zhang Xiaowen Wang Yaru Lian Bin Guo Miao Han Xiaoe Zhang Xiaoting Zhu Sixian Xu Zengli Guo Yunli Bi Qian Shen Xiang Wang Jiaojiao Liu Yuan Zhuang Ting Ni Hong Xu Xiaohui Wu

Congenital anomalies of the kidney and urinary tract (CAKUT) are among the most common developmental defects in humans. Despite of several known CAKUT-related loci (HNF1B, PAX2, EYA1, etc.), the genetic etiology of CAKUT remains to be elucidated for most patients. In this study, we report that disruption of the Holliday Junction resolvase gene Gen1 leads to renal agenesis, duplex kidney, hydron...

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