A lot of diseases, including lupus profundus, morphea, lipodystrophy, and Parry-Romberg syndrome, may manifest progressive hemifacial atrophy. These diseases usually progress slowly and rapid progression of atrophy is extremely rare. We report a case of elderly-onset rapid progression of hemifacial atrophy only in three weeks. Our case did not meet variable differential diagnoses. We discuss th...

Progressive facial hemiatrophy or Parry-Romberg Syndrome is a rare disease characterized by atrophy in subcutaneous tissues on skin on one half of the face and some accompanied systematic findings. Generally, it develops before the age of 20. It is quite difficult to discriminate it from linear scleroderma localized in fronto-parietal area as they have similar clinical characteristics. In this ...

Parry-Romberg syndrome is a rare disease characterized by progressive hemifacial atrophy associated with other systemic changes, including neurological symptoms. Currently, there are few studies exploring the utilization of advanced magnetic resonance sequences in the investigation of this disease. The authors report the case of a 45-year-old patient and describe the findings at structural magn...

Parry-Romberg Syndrome (PRS) is a rare condition manifesting in severe progressive hemifacial atrophy involving skin, soft tissue, and bone [1]. It is often found in the first decade of life, usually in females. It can cause severe facial pain and is associated with other autoimmune disorders and inflammatory changes noted on MRI [2]. Although many have studied its etiology and the complexities...

BACKGROUND Hemifacial atrophy (Parry-Romberg syndrome) is a relatively rare disease. The etiology of the disease is not clear. Some authors postulate its relation with limited scleroderma linearis. Linear scleroderma "en coup de sabre" is characterized by clinical presence of most commonly one-sided linear syndrome. In a number of patients, neurological affection is the medium of the disease. T...

Acta Neurologica Taiwanica Vol 13 No 4 December 2004 From the Department of Neurology, Chang Gung Memorial Hospital, Linkou Medical Center, Taoyuan, Taiwan. Received November 19, 2004. Revised and Accepted November 29, 2004. Reprint requests and correspondence to: Nai-Shin Chu, MD. Department of Neurology, Chang Gung Memorial Hospital, No. 199, Tung-Hwa N. Road, Taipei, Taiwan. E-mail: chu060@c...