نتایج جستجو برای: mycn

تعداد نتایج: 1228  

Journal: :Cancer research 1990
L Schweigerer S Breit A Wenzel K Tsunamoto R Ludwig M Schwab

Amplification and enhanced expression of the MYCN oncogene are thought to contribute to the development and progression of human neuroblastomas. Here, we have transfected human neuroblastoma cells that harbor a single MYCN gene copy with the human MYCN gene driven by a viral enhancer/promoter, and we have compared the properties of the parental and the transfected cells. The transfected cells s...

Journal: :International journal of oncology 2008
Juergen Becker Sonja Volland Ievgeniia Noskova Alexander Schramm Lothar L Schweigerer Joerg Wilting

Neuroblastoma is the most frequent solid malignancy of children. The most reliable prognostic factor in neuroblastoma is the amplification status of the MYCN oncogene, but exceptions from this rule have been observed. Recently we have demonstrated that keratoepithelin (BIGH3, TGFBI) expression significantly reduces proliferation and invasion of neuroblastomas in vitro and in vivo. In these expe...

2013
Candy Kumps Annelies Fieuw Pieter Mestdagh Björn Menten Steve Lefever Filip Pattyn Sara De Brouwer Tom Sante Johannes Hubertus Schulte Alexander Schramm Nadine Van Roy Tom Van Maerken Rosa Noguera Valérie Combaret Christine Devalck Frank Westermann Geneviève Laureys Angelika Eggert Jo Vandesompele Katleen De Preter Frank Speleman

Neuroblastoma is an embryonic tumor arising from immature sympathetic nervous system cells. Recurrent genomic alterations include MYCN and ALK amplification as well as recurrent patterns of gains and losses of whole or large partial chromosome segments. A recent whole genome sequencing effort yielded no frequently recurring mutations in genes other than those affecting ALK. However, the study f...

2011
Marta Terrile Kenneth Bryan Lynsey Vaughan Albert Hallsworth Hannah Webber Louis Chesler Raymond L. Stallings

BACKGROUND MicroRNAs are small molecules which regulate gene expression post-transcriptionally and aberrant expression of several miRNAs is associated with neuroblastoma, a childhood cancer arising from precursor cells of the sympathetic nervous system. Amplification of the MYCN transcription factor characterizes the most clinically aggressive subtype of this disease, and although alteration of...

2015
Zai Ahmad Lukasz Jasnos Veronica Gil Louise Howell Albert Hallsworth Kevin Petrie Tomoyuki Sawado Louis Chesler

Medulloblastoma (MB) is the most common malignant pediatric brain tumor. While the pathways that are deregulated in MB remain to be fully characterized, amplification and/or overexpression of the MYCN gene, which is has a critical role in cerebellar development as a regulator of neural progenitor cell fate, has been identified in several MB subgroups. Phenotypically, aberrant expression of MYCN...

Journal: :The Journal of clinical investigation 2018
Liying Chen Gabriela Alexe Neekesh V Dharia Linda Ross Amanda Balboni Iniguez Amy Saur Conway Emily Jue Wang Veronica Veschi Norris Lam Jun Qi W Clay Gustafson Nicole Nasholm Francisca Vazquez Barbara A Weir Glenn S Cowley Levi D Ali Sasha Pantel Guozhi Jiang William F Harrington Yenarae Lee Amy Goodale Rakela Lubonja John M Krill-Burger Robin M Meyers Aviad Tsherniak David E Root James E Bradner Todd R Golub Charles Wm Roberts William C Hahn William A Weiss Carol J Thiele Kimberly Stegmaier

Pharmacologically difficult targets, such as MYC transcription factors, represent a major challenge in cancer therapy. For the childhood cancer neuroblastoma, amplification of the oncogene MYCN is associated with high-risk disease and poor prognosis. Here, we deployed genome-scale CRISPR-Cas9 screening of MYCN-amplified neuroblastoma and found a preferential dependency on genes encoding the pol...

2017
Kathryn G Ewens Tricia R Bhatti Kimberly A Moran Jennifer Richards-Yutz Carol L Shields Ralph C Eagle Arupa Ganguly

A small, but unique subgroup of retinoblastoma has been identified with no detectable mutation in the retinoblastoma gene (RB1) and with high levels of MYCN gene amplification. This manuscript investigated alternate pathways of inactivating pRb, the encoded protein in these tumors. We analyzed the mutation status of the RB1 gene and MYCN copy number in a series of 245 unilateral retinoblastomas...

Journal: :International journal of cancer 2012
Sara De Brouwer Pieter Mestdagh Irina Lambertz Filip Pattyn Anne De Paepe Frank Westermann Christina Schroeder Johannes H Schulte Alexander Schramm Katleen De Preter Jo Vandesompele Frank Speleman

Neuroblastoma (NB) is a paediatric tumour with a remarkable diverse clinical behaviour. Approximately half of the high stage aggressive tumours are characterized by MYCN gene amplification but our understanding of the role of MYCN in NB oncogenesis is incomplete. Previous studies have shown that MYCN expression is inversely correlated with expression of Dickkopf-3 (DKK3), a gene encoding an ext...

2011
Derek M. Murphy Patrick G. Buckley Sudipto Das Karen M. Watters Kenneth Bryan Raymond L. Stallings

BACKGROUND MYCN is a transcription factor that is expressed during the development of the neural crest and its dysregulation plays a major role in the pathogenesis of pediatric cancers such as neuroblastoma, medulloblastoma and rhabdomyosarcoma. MeCP2 is a CpG methyl binding protein which has been associated with a number of cancers and developmental disorders, particularly Rett syndrome. MET...

Journal: :Clinical cancer research : an official journal of the American Association for Cancer Research 2007
Frank Westermann Kai-Oliver Henrich Jun S Wei Werner Lutz Matthias Fischer Rainer König Ruprecht Wiedemeyer Volker Ehemann Benedikt Brors Karen Ernestus Ivo Leuschner Axel Benner Javed Khan Manfred Schwab

PURPOSE Amplified MYCN oncogene defines a subgroup of neuroblastomas with poor outcome. However, a substantial number of MYCN single-copy neuroblastomas exhibits an aggressive phenotype similar to that of MYCN-amplified neuroblastomas even in the absence of high MYCN mRNA and/or protein levels. EXPERIMENTAL DESIGN To identify shared molecular mechanisms that mediate the aggressive phenotype i...

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