Uterus didelphys with obstructed hemivagina and ipsilateral renal agenesis (OHVIRA Syndrome) is a rare congenital anomaly of the female genital tract. Uterus didelphys occurs when the midline fusion of the mullerian ducts is arrested, either completely or incompletely. Women with didelphic uterus may be asymptomatic and unaware of having a double uterus. They may present with complaints of dysm...

Herlyn – Werner – Wunderlich syndrome (HWWS) is an uncommon combined Mullerian and Mesonephric duct anomaly, and its presentation in neonatal period is even rarer. Symptoms generally occur after menarche about 12 to 13 years old and it is usually diagnosed by pelvic magnetic resonance imaging. Our case is 1 day old asymptomatic newborn with all the features of this syndrome that came to our att...

The uterus is formed during embryogenesis by the fusion of the two paramesonephric ducts (also called mullerian ducts). This process usually fuses the two mullerian ducts into a single uterine body. Incomplete fusion of the mullerian ducts results in uterine malformation like uterus didelphus, uterus bicornis bicollis, uterus bicornis unicollis, uterus subseptate, uterus arcuate, and uterus uni...

Received January 2008 Accepted October 2008 INTRODUCTION Persistent mullerian duct syndrome (PMDS), or hernia uteri inguinale, describes a group of patients with a 46,XY karyotype and normal male external genitalia, but internal mullerian duct structures. Typically, these phenotypic males have unilateral or bilateral undescended testes, bilateral fallopian tubes, a uterus, and an upper vaginal ...

Previous studies using cDNA microarray have indicated that distinct gene expression profiles characterize endometrioid and papillary serous carcinomas of the endometrium. Molecular studies have observed that mixed mullerian tumors, characterized by both carcinomatous and sarcomatous components, share features that are characteristic of endometrial carcinomas. The objective of this analysis was ...

The presence of cervicovaginal agenesis with unicornuate uterus is a very rare mullerian anomaly. Its true incidence is still unknown. The presence of functioning unicornuate uterus poses a great challenge for a gynecologist because a successful repair could restore normal menses and may preserve a patient's fertility. Hence, we report a case of 16-year-old unmarried female who presented with c...

BACKGROUND Congenital uterine malformations are the result of disturbances in mullerian duct development. In patients with recurrent miscarriage, the reported frequency of uterine anomalies varies widely, from 1.8% to 37.6%. There are reports in which cervical cerclage has been shown to prevent preterm labor in uterine anomalies. The aim of this study was to compare the role of cervical cerclag...

Persistent Mullerian Duct Syndrome (PMDS), a rare form of male pseudohermaphroditism. It is characterized by the persistence of Mullerian duct structures (uterus, fallopian tubes and upper two-thirds of vagina) in otherwise normally virilized males (Karyotype 46XY). The exact cause of PMDS is not known, however it is thought to result from the defect of the synthesis or release of Mullerian inh...

mullerian duct anomalies (mdas) are relatively common disorders that are particularly responsible for obstetrical complications and have a prevalence of about 3%-4% in the general population (1, 2). uterine malformations may result from arrested development of the mullerian ducts, failure of fusion of the mullerian ducts or failure of resorption of the median septum (1, 2).