Mailing Address: Edmar Atik • InCor – Av. Dr Enéas C. Aguiar, 44 – 05403-000 – São Paulo, SP, Brazil E-mail: [email protected] Clinical data A three-year-old white female who had been previously diagnosed by echocardiography as having Tetralogy of Fallot with perimembranous ventricular septal defect (VSD) and infundibular pulmonary stenosis after a heart murmur was detected in a routine exam...

In contrast with transthoracic echocardiography, transesophageal echocardiography provides a sure way to make the diagnosis of sinus venosus atrial septal defect; on the other hand this abnormality is more complex than that seen with the secundum atrial septal defect, and inexperienced operators may fail to recognize properly the defect. In front of a high reported sensitivity using transesopha...

OBJECTIVE In this study, we tested 3 techniques of atrial septal defect closure under real-time 3-dimensional echocardiography guidance in a swine model. METHODS The operations were conducted under the sole guidance of a modified real-time 3-dimensional echocardiography guidance system with a x4 matrix transducer (Sonos 7500, Philips Medical Systems, Andover, Mass). Eighteen swine were anesth...

INTRODUCTION Aortopulmonary window (APW), a large aortopulmonary septal defect (APSD), is a serious and rare defect within congenital heart diseases. CASE REPORT In this study, we reported an APW case with severe pulmonary arterial hypertension. This patient was successfully treated by transcatheter closure with a muscular ventricular septal defect (VSD) occluder. CONCLUSION We had a succes...

Introduction Holt & Oram (1960) linked various skeletal abnormalities with congenital heart disease in four generations of a family. In particular, malformations of the hands were associated with atrial septal defect (secundum type) and bizarre arrhythmias. In 1961, McKusick described a similar syndrome in a mother and daughter and suggested the term 'atrio-digital dysplasia'. Harris & Osborne ...

OBJECTIVE To analyse the spectrum of congenital heart malformations, the frequency of extracardiac malformations, and the proportion of chromosome aberrations among fetuses sent for necropsy. MATERIAL Necropsies were performed on 815 fetuses-448 induced abortions (55%), 220 spontaneous abortions (27%), and 147 stillbirths (18%)-during a seven year period (1991-97) in the department of patholo...

IN PATIENTS with ventricular septal defect who are more than 3 or 4 years of age, an open corrective operation may be carried out with minimal risk if the lesion is not complicated by the presence of severe pulmonary hypertension. With surgical technics presently available, however, the closure of a ventricular septal defect in an infant or very young child is associated with considerable hazar...

IN PATIENTS with ventricular septal defect who are more than 3 or 4 years of age, an open corrective operation may be carried out with minimal risk if the lesion is not complicated by the presence of severe pulmonary hypertension. With surgical technics presently available, however, the closure of a ventricular septal defect in an infant or very young child is associated with considerable hazar...

Double-chambered right ventricle (DCRV) is a rare congenital heart disorder involving 2 different right ventricle (RV) pressure compartments that is often associated with ventricular septal defect (VSD). Usually, the obstruction is caused by an anomalous muscle bundle crossing the RV from the interventricular septum to the RV free wall. We are reporting a case of double-chambered right ventricl...

A secundum atrial septal defect is the most common congenital heart defect. Transcatheter treatment of secundum atrial septal defects is a popular and less invasive alternative to surgery. Procedural complications may occur in a wide spectrum, particularly device embolus as the most emergent one, but luckily they do not commonly occur in the clinical setting. Mortality from adverse events relat...