The authors present the case of three patients from the same family in whom hereditary hemorrhagic telangiectasia (HHT) or Rendu-Osler-Weber syndrome was diagnosed. The disease is rare and occurs with multiple telangiectases of the skin and mucosa, and pulmonary arteriovenous fistulae. The clinical status of our patients included multiple telangiectases of the skin and mucosa, recurrent epistax...

Received 2/2/2007; revised 4/2/2007; accepted 4/3/2007. For correspondence or reprints contact: Chiung-Zuan Chiu, M.D., Division of Cardiology, Shin-Kong Wu Ho-Su Memorial Hospital. 95 Wen Chan Road, Shih Lin, Taipei 111, Taiwan. Tel: (886)2-28332211 ext. 9456, Fax: (886)2-28123397, E-mail: [email protected] Background: Coronary fistula is a congenital anomaly resulting in steal phenomenon o...

Aortoenteric fistulae are life-threatening conditions characterized by abnormal communications between the aorta and gastrointestinal tract. Aortoenteric fistulae may be characterized by the triad of bleeding, abdominal pain, or a pulsatile abdominal mass. Although hemorrhage is the most common presentation, it does not always occur; thus, patients may present with nonspecific symptoms. Compute...

UNLABELLED Anal fistula is a benign inflammatory disease with unclear etiology which develops in approximately 10 in 100 000 adult patients. Surgical treatment of fistulae is associated with a risk of damaging anal sphincters. This usually happens in treating high fistulae, branched fistulae, and anterior ones in females. In preoperative diagnosis of anal fistulae, endosonography and magnetic r...

Coronary fistulae and ventricular septal perforation are very rare clinically, and even less caused by cardiac leiomyosarcoma. A case is reported that a 67-year-old female had cardiac leiomyosarcoma with progressive heart failure and coronary fistulae and ventricular septal perforation. This case was special since all ante-mortem examinations and cardiac surgery failed to detect the presence of...

introduction: while the development of fistulae is a well-known complication of radiotherapy, such fistulae can often be challenging to manage. case presentation: we describe the case of a 37 year old male who developed in succession a urethrocutaneous fistula to the thigh, a rectourethral fistula and a peritoneo-urethral fistula 35 years after radiotherapy for pediatric pelvic rhabdomyosarcoma...

Dural arteriovenous fistulae of the transverse and sigmoid sinuses are highly variable in symptomatology and prognosis. However, we have identified a subgroup of patients who have a high risk of hemorrhage and dementia due to severe venous overload caused by high arterial flow into the fistulae and by occlusive changes of the transverse and sigmoid sinuses. Three representative cases selected f...

Congenital pulmonary arteriovenous fistulae, provided that they are not present in very large numbers, are best managed surgically, and there is no effective alternative management. Where pulmonary arteriovenous fistulae develop as a consequence of pulmonary hypertension it is rational to resect the fistulae if the cause of pulmonary hypertension - for example, mitral stenosis - is correctable....

BACKGROUND AND OBJECTIVES Given different sites of stenosis and access blood flow rates (Qa), the criteria for diagnosing fistula stenosis might vary according to anastomotic site. To test this, we analyzed the database of a prospective blinded study seeking an optimal bedside screening program for fistula stenosis. DESIGN, SETTING, PARTICIPANTS, & MEASUREMENTS Several methods used during dia...

UNLABELLED This study provides the long-term follow-up data on the efficacy of infliximab in the treatment of chronic refractory pouchitis complicated by fistulae following ileo-pouch anal anastomosis (IPAA) for ulcerative colitis (UC). METHODS Seven patients (4 F, 3 M) with chronic refractory pouchitis complicated by fistulae were included in an open study. Pouchitis was diagnosed by clinica...