Cystic fibrosis (CF) is a multisystemic disease but without a classical disease-specific renal phenotype. A 32-year-old male patient with CF (ΔF508/ΔF508) presented with a nephrotic syndrome. Renal biopsy revealed nodular glomerulosclerosis (NGS) occurring in the absence of diabetes mellitus, amyloidosis and any other known common cause of NGS. He had a progressive decline in estimated glomerul...

Chemical inhibdion of dtiusion flames through addition of halogenatkd “inhibitors is a problem of significant practical and scientific interest. Extensive studies on diffusion flames in microgravity have shown that these flames have significantly different characteristics than those under normal gravity [1,2]. However, the mechanisms through which inhibitors reach the reaction zone to suppress ...

Achromobacter spp. are recognized as emerging pathogens in hospitalized as well as in cystic fibrosis (CF) patients. From 2012 to 2015, we collected 69 clinical isolates (41 patient) of Achromobacter spp. from 13 patients with CF (CF isolates, n = 32) and 28 patients receiving care for other health conditions (non-CF isolates, n = 37). Molecular epidemiology and virulence potential of isolates ...

In patients with cystic fibrosis (CF) and non-CF bronchiectasis, Pseudomonas aeruginosa is the most important respiratory pathogen. It is able to synthesise hydrogen cyanide, a potent inhibitor of cellular respiration. The present study investigated whether cyanide is present in the sputum of CF and non-CF bronchiectasis patients infected with P. aeruginosa, and whether the detection of cyanide...

stereoisograms of octahedral complexes are classified into five types (type i--typev) under the action of the corresponding rs-stereoisomeric group. their enumeration is accomplished in a type-itemized fashion, where fujita's proligand method developed originally for combinatorial enumeration under point groups (s. fujita, theor. chem. acc., 113, 73--79 (2005)) is extended to meet the requireme...

background: cystic fibrosis (cf) is a common genetic disorder chiefly characterized by respiratory and gastrointestinal symptoms. the purpose of this study was to evaluate the clinical presentation and growth status in cf patients at the time of diagnosis and following conventional treatment. materials and methods: a cross-sectional study was conducted on 67 cf patients who enrolled for at leas...

Abstract Background Different gamma camera calibration factor (CF) geometries have been proposed to convert SPECT data into units of activity concentration. However, no consensus has reached on a standardised geometry. The CF is dependent the selected geometry and further affected by partial volume effects. This study investigated effect two their corresponding recovery coefficients (RCs) quant...

To understand the role of religiousness/spirituality in coping in children with cystic fibrosis (CF). Participants were a convenience sample of 23 patients with CF, ages 5 to 12 years and their parent(s) in an ambulatory CF clinic. The design was a focused ethnography including in-depth interviews with children and parent(s), children’s drawings and self-administered written parental questionna...

NORTHWEST AFRICA 5790. TOP SEQUENCE OF THE NAKHLITE PILE. A. Jambon J-A. Barrat2,3, C. Bollinger2,3, V. Sautter4, O. Boudouma1 , R.C. Greenwood5, I.A. Franchi5 and D. Badia1, 1UPMC Univ Paris 06, ISTEP CNRS-UMR 7193, Paris France [email protected] , 2Université Européenne de Bretagne, 3Université de Brest CNRS-UMR 6538 IUEM, 29280 Plouzané France, MNHN Paris, Laboratoire de Minéralogie et C...