نتایج جستجو برای: x linked agammaglobulinemia

تعداد نتایج: 830153  

Journal: :Blood 1998
T Futatani T Miyawaki S Tsukada S Hashimoto T Kunikata S Arai M Kurimoto Y Niida H Matsuoka Y Sakiyama T Iwata S Tsuchiya O Tatsuzawa K Yoshizaki T Kishimoto

The B-cell defect in X-linked agammaglobulinemia (XLA) is caused by mutations in the gene for Bruton's tyrosine kinase (BTK). Using the anti-BTK monoclonal antibody (48-2H), a flow cytometric analysis of intracytoplasmic BTK protein expressed in monocytes was successfully performed. To examine the possible identification of XLA patients and female carriers by this assay, we studied 41 unrelated...

2015
S. Haessler T. Balčiūnas G. Fan L. E. Chipperfield A. Baltuška

Isolated attosecond pulses (IAP) generated by high-order harmonic generation are valuable tools that enable dynamics to be studied on the attosecond time scale. The applicability of these IAP would be widened drastically by increasing their energy. Here we analyze the potential of using multi-colour driving pulses for temporally gating the attosecond pulse generation process. We devise how this...

2017
Filomena Monica Cavaliere Alessandro Prezzo Caterina Bilotta Metello Iacobini Isabella Quinti

The lack of BTK in X-linked agammaglobulinemia (XLA) patients does not affect monocytes and polymorphonuclear cells (PMN) phenotype and functions. In this study, we show that XLA patients had an increased frequency of the intermediate monocytes subset and that BTK-deficient monocytes and PMN had a normal expression of receptors involved in the activation and cellular responses. We demonstrate t...

2011
Sukesh Sukumaran Katherine Marzan Bracha Shaham Joseph A. Church

X-linked agammaglobulinemia (XLA) is a primary immune deficiency characterized by recurrent bacterial infections and profoundly depressed serum immunoglobulin levels and circulating mature B cells. We describe a 12-year-old boy with XLA and enthesitis-related arthritis (ERA). To date, there has been a paucity of reports of noninfectious inflammatory arthritis in children with XLA. This case ill...

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