Portal biliopathy is the complex of abnormalities of extrahepatic and intrahepatic bile ducts, cystic duct, and gallbladder, arising as a result of extrahepatic portal vein obstruction and noncirrhotic portal fibrosis, which can be caused by coagulopathies, tumors, inflammation, postoperative complications, dehydration, and neonatal umbilical vein catheterization. We report a case of a 55-year-...

Urinary ascites from bladder perforation in neonate is a rare event reported to occur more commonly following umbilical artery catheterization. Other causes include bladder perforations in neonates with bladder abnormalities, following bladder instrumentation or idiopathic bladder perforations. The present manuscript describes a full-term female neonate with spontaneous bladder perforation who ...

Congenital abnormalities were present in 12 out of 30 (40%) children with extrahepatic portal hypertension of unknown cause, but in only 2 out of 17 (12%) children with extnahepatic portal hypertension secondary to umbilical vein catheterization or omphalitis. The most frequent abnormalities in this series and in published reports were atrial septal defect, malformation of the biliary tract, an...

hypertension in newborn infants, particularly those requiring intensive care, is becoming increasingly recognized, with prevalence of 0.2-3%. recent studies have established normative tables for blood pressure (bp) in both term and pre-term infants based on the gestational age, postnatal age, gender, weight and height, identifying the neonates at increased risk for early-onset cardiovascular di...

Case report An eight year old boy presented with polyuria and polydipsia for 1 month. On examination, liver was not palpable but spleen was enlarged (6cm). Blood sugar was 460 mg/dl and type1 DM was confirmed. Ultrasonography showed portal vein cavernoma with normal liver and pancreas. Endoscopy revealed grade 2 esophageal varices. Thus diagnosis of EHPVO with portal hypertension was also confi...