A patient with very long chain acyl-CoA dehydrogenase (VLCAD) deficiency is reported. He had a severe neonatal presentation and cardiomyopathy. He was found to be homozygous for a severe mutation with no residual enzyme activity. Tandem mass spectrometry on dried blood spots revealed increased long chain acylcarnitines. VLCAD enzyme activity was severely decreased to 2% of control levels. Dieta...

Milk cream is a fluid milk product comparatively rich in fat, the form of an emulsion fat-in-skimmed milk, obtained by physical separation from and widely used food industry. This study aims to evaluate consequences ozone treatment exposure time on lipid oxidation cream, using peroxide value (PV) thiobarbituric acid reactive substances (TBARS) methods. Ozonation process significantly affects PV...

BACKGROUND:Due to the large proportion of iodine present in milk and dairy products, they have been one of the important sources of nutritional iodine in several countries. Information about variation in milk iodine concentration in Iran is limited. OBJECTIVES:The present study was conducted to determine the iodine concentration in Iranian milk and dairy ...

Lyophilization, the removal of water by freezing and then volatilization at low pressure and temperature, has been employed as a standard long-term preservation method for many filamentous fungi. The method outlined involves the use of standard shelf freeze-drying and skimmed milk as a suspending solution/lyoprotectant. This approach has been employed to freeze-dry the majority of the 50,000 fu...

Milk is one of the primary animal-based foods in a healthy diet which provides vitamins, fats and particularly calcium to meet daily requirements. Currently, there are limited number metabolomics studies on milk more required establish reliable international standards databases for metabolite profiles. In this study, analysis three types UHT whole-milk, semi-skimmed lactose-free from Türkiye wa...

Stunting is one of the public health problems that has yet to be solved in Indonesia. This study developed synbiotic fermented milk with iron and zinc fortification was then tested a clinical setting. The product made from skimmed fructooligosaccharides (FOS) Lactobacillus plantarum. A sample 94 stunted children under five years old were randomly assigned intervention or control groups. group r...

UNLABELLED Vitamin D exerts a variety of extra-skeletal functions. AIM to know the effects of the consumption of a vitamin D-fortified skimmed milk on glucose, lipid profile, and blood pressure in young women. METHODS a randomised, placebo-controlled, double-blind parallel-group trial of 16 weeks duration was conducted in young women with low iron stores who consumed a skimmed milk fortifie...