We present a rare case of hemoptysis secondary to isolated unilateral pulmonary vein atresia. Isolated pulmonary vein atresia is a rare condition in which patients typically acquire a diagnosis in infancy and early childhood [Mataciunas et al.; Pourmoghadam et al.]. Our patient presented during puberty with several previous episodes of hemoptysis prior to her admission and diagnosis. The initia...

Bronchial atresia is a rare pulmonary anomaly characterized by a blindly-terminating bronchus, mucoid impaction, and hyperinflation of the obstructed segment of the lung.1 Chest radiographic findings typically show mucoid impaction, segmental overinflation, and hypovascularity, although most patients do not have any respiratory symptoms.1,2 We herein present 2 cases of bronchial atresia with un...

Rev Esp Cardiol 2002;55(6):671-2 671 Congenital atresia of the pulmonary veins is a rare anomaly that is not associated with other heart disease. It has a poor prognosis and patients die secondary to pulmonary hypertension, recurrent hemoptysis, pulmonary edema, or congestive cardiac insufficiency. We present a 5-year-old male patient admitted to the hospital for asthenia, anorexia, hemoptoic v...

In order to establish a normal, in-series circulation physiologically, very different from the circulation in parallel which the children are born with single ventricle, doctors Fontan and Baudet (2) and Kreutzer (3) concurrently developed surgical treatment of patients with tricuspid atresia to achieve a passive flow through the pulmonary vascular bed (1). Management strategies for patients wi...

OBJECTIVES To determine the effect and safeness of the right ventricle to pulmonary artery connection with occlusion of major aortopulmonary collaterals and pulmonary artery angioplasty to rehabilitate the hypoplastic pulmonary arteries in patients with pulmonary atresia and ventricular septal defect beyond the infant period. METHODS From December 2009 to August 2012, 37 consecutive patients ...

Two cases of common pulmonary vein atresia (CPVA) are presented. In one, the diagnosis was suspected on clinical grounds, and in both it was c onfirmed by cardiac catheterization and angiocardiography. Surgical correction was attempted unsuccessfully in one. Prompt identification of the defect followed by immediate operation, using a technic of profound hypothermia and circulatory arrest, offer...

In a patient with pulmonary valve atresia with hypoplastic main pulmonary artery selective angiography showed absence of the central left pulmonary artery and a right pulmonary artery originating from the ascending aorta close to the left coronary artery. This unusual anatomical arrangement complicates interventional and surgical treatment.

the present report describes a male newborn with a pulsatile structure beneath the sternum. echocardiography showed common atrium, a single ventricle, mitral atresia, double outlet right ventricle, subpulmonary stenosis, small pulmonary artery branches, and a thin walled ventricular diverticulum suggestive of cantrell's syndrome. the diverticulum was resected to prevent life threatening events ...

Method 2013-2014: 23 congenital cardiac patients underwent heart transplantation. 13 of them: previous univentricular palliation: hypoplastic left heart syndrome (n = 8), dtransposition of great arteries+criss-cross-heart (n = 1), unbalanced atrioventricular septal defect (n = 1), pulmonary atresia+intact ventricular septum (n = 1) and grown-up patients (GUCH) (n = 2: 1 double-inlet-leftventric...

Fifty-six patients with tricuspid atresia and decreased pulmonary blood flow received a systemic-to-pulmonary artery anastomosis as a preliminary operation. Thirty-five had a Waterston shunt, 12 a Blalock-Taussig anastomosis, and nine various other procedures. The age at operation ranged from 2 days to 10 years (median 4.5 months). Pulmonary atresia was present in eight newborn infants. Four pa...