نتایج جستجو برای: nphs2 protein

تعداد نتایج: 1234819  

Journal: :Saudi Journal of Kidney Diseases and Transplantation 2013

Journal: :Internal medicine 2010
Min-shu Zou Jian Yu Jian-hua Zhou Guo-ming Nie Dong-sheng Ding Li-man Luo Hong-tao Xu Wei-sun He

OBJECTIVE To investigate the role of α3β1 integrin and α/β-dystroglycan in protective effects of 1,25(OH)2D3 on podocytes in rats with adriamycin-induced nephropathy. METHODS Sprague-Dawley rats were randomly divided into three groups: control group (NC), nephropathy group (NE), and nephropathy+1,25(OH)2D3 group (ND). Rats in NE and ND group were injected intravenously with adriamycin (0.1 mg...

Journal: :Journal of the American Society of Nephrology : JASN 2003
Klaas Koop Michael Eikmans Hans J Baelde Hiroshi Kawachi Emile De Heer Leendert C Paul Jan A Bruijn

Proteinuria is a poorly understood feature of many acquired renal diseases. Recent studies concerning congenital nephrotic syndromes and findings in genetically modified mice have demonstrated that podocyte molecules make a pivotal contribution to the maintenance of the selective filtration barrier of the normal glomerulus. However, it is unclear what role podocyte molecules play in proteinuria...

Journal: :Molecular and cellular biology 2003
Tobias B Huber Björn Hartleben Jeong Kim Miriam Schmidts Bernhard Schermer Alexander Keil Lotti Egger Rachel L Lecha Christoph Borner Hermann Pavenstädt Andrey S Shaw Gerd Walz Thomas Benzing

Mutations of NPHS1 or NPHS2, the genes encoding nephrin and podocin, as well as the targeted disruption of CD2-associated protein (CD2AP), lead to heavy proteinuria, suggesting that all three proteins are essential for the integrity of glomerular podocytes, the visceral glomerular epithelial cells of the kidney. It has been speculated that these proteins participate in common signaling pathways...

2012
Yanchun Qu E Du Yue Zhang Shengzhi Li Ruifa Han Mengsheng Qiu

BACKGROUND Bone morphogenetic protein 7 (BMP7) has been suggested to play a protective role against kidney injury in chronic kidney disease. OBJECTIVES To identify the critical molecular regulators in the early stage of diabetic nephropathy, we studied the expression of BMP7 and 2 important kidney-specific markers, podocin and Tamm-Horsfall protein (THP). MATERIALS AND METHODS A diabetic ne...

Journal: :Journal of the American Society of Nephrology : JASN 2002
Michelle P Winn

The causes of familial nephrotic syndromes are varied and diverse. Although phenotypic differences are seen with distinct congenital and adult forms, renal pathology tends to be less well defined, with blurring and overlap of diagnoses. Clinically, symptoms of the familial nephrotic syndromes may appear from birth to late in life, which demonstrates the heterogeneity of these diseases. The dise...

Journal: :Journal of medical genetics 2010
Olivia Boyer Geneviève Benoit Olivier Gribouval Fabien Nevo Audrey Pawtowski Ilmay Bilge Zelal Bircan Georges Deschênes Lisa M Guay-Woodford Michelle Hall Marie-Alice Macher Kenza Soulami Constantinos J Stefanidis Robert Weiss Chantal Loirat Marie-Claire Gubler Corinne Antignac

BACKGROUND Mutations in the PLCE1 gene encoding phospholipase C epsilon 1 (PLCepsilon1) have been recently described in patients with early onset nephrotic syndrome (NS) and diffuse mesangial sclerosis (DMS). In addition, two cases of PLCE1 mutations associated with focal segmental glomerulosclerosis (FSGS) and later NS onset have been reported. METHOD In order to better assess the spectrum o...

2014
Yu Sun Hongxia Zhang Ruimin Hu Jianyong Sun Xing Mao Zhonghua Zhao Qi Chen Zhigang Zhang

Growing evidence suggests that there are many common cell biological features shared by neurons and podocytes; however, the mechanism of podocyte foot process formation remains unclear. Comparing the mechanisms of process formation between two cell types should provide useful guidance from the progress of neuron research. Studies have shown that some mature proteins of podocytes, such as podoci...

Journal: :Nephrology Dialysis Transplantation 2007

Journal: :Genetics and molecular research : GMR 2014
D N Feng Y H Yang D J Wang D C Meng R Fu J J Wang Z H Yu

Recent studies have demonstrated that mutations in 4 podocyte genes, NPHS1, NPHS2, CD2AP, and WT1, are associated with the pathogenesis of steroid-resistant nephrotic syndrome (SRNS). Systematic investigation of all 4 genes for sporadic SRNS in China has not been performed. We examined 10 Chinese children with sporadic SRNS who showed no response to immunosuppressive agents and 20 SRNS controls...

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