نتایج جستجو برای: mitochondrial respiratory chain complex i

تعداد نتایج: 2265450  

Journal: :Carcinogenesis 2003
Helene Simonnet Jocelyne Demont Kathy Pfeiffer Leila Guenaneche Raymonde Bouvier Ulrich Brandt Hermann Schagger Catherine Godinot

Renal oncocytomas are benign tumors characterized by dense accumulation of mitochondria the cause of which remains unknown so far. Consistently, mitochondrial DNA content and the amounts and catalytic activities of several oxidative phosphorylation (OXPHOS) complexes were known to be increased in these tumors, but it was not ascertained that the OXPHOS system was functional. Here we investigate...

Journal: :journal of research in medical sciences 0
gui-lang zheng juan-juan lyu mei-yan xie jing-da huang dan xiang qi-yi zeng

sepsis is a systemic inflammatory response to infection. sepsis, which can lead to severe sepsis, septic shock, and multiple organ dysfunction syndrome, is an important cause of mortality. pathogenesis is extremely complex. in recent years, cell hypoxia caused by mitochondrial dysfunction has become a hot research field. sepsis damages the structure and function of mitochondria,conversely, mito...

Journal: :The European journal of neuroscience 2002
Alexei P Kudin Tatiana A Kudina Jan Seyfried Stefan Vielhaber Heinz Beck Christian E Elger Wolfram S Kunz

Mitochondrial function is a key determinant of both excitability and viability of neurons. Here, we demonstrate seizure-dependent changes in mitochondrial oxidative phosphorylation in the epileptic rat hippocampus. The intense pathological neuronal activity in pilocarpine-treated rats exhibiting spontaneous seizures resulted in a selective decline of the activities of NADH-CoQ oxidoreductase (c...

2017
Lingmei Sun Kai Liao Dayong Wang

BACKGROUND Honokiol, a compound extracted from Magnolia officinalis, has antifungal activities by inducing mitochondrial dysfunction and triggering apoptosis in Candida albicans. However, the mechanism of honokiol-induced oxidative stress is poorly understood. The present investigation was designed to determine the specific mitochondrial reactive oxygen species (ROS)-generation component. MET...

Journal: :JAMA neurology 2015
Michela Ripolone Dario Ronchi Raffaella Violano Dionis Vallejo Gigliola Fagiolari Emanuele Barca Valeria Lucchini Irene Colombo Luisa Villa Angela Berardinelli Umberto Balottin Lucia Morandi Marina Mora Andreina Bordoni Francesco Fortunato Stefania Corti Daniela Parisi Antonio Toscano Monica Sciacco Salvatore DiMauro Giacomo P Comi Maurizio Moggio

IMPORTANCE The important depletion of mitochondrial DNA (mtDNA) and the general depression of mitochondrial respiratory chain complex levels (including complex II) have been confirmed, implying an increasing paucity of mitochondria in the muscle from patients with types I, II, and III spinal muscular atrophy (SMA-I, -II, and -III, respectively). OBJECTIVE To investigate mitochondrial dysfunct...

Journal: :Clinical chemistry 1993
N Barroso Y Campos R Huertas J Esteban J A Molina A Alonso E Gutierrez-Rivas J Arenas

Respiratory chain enzyme activities were studied in lymphocytes from patients with Parkinson disease (PD) (n = 16) and age-matched control subjects (n = 15). The patients had received no therapy before the study was conducted. Complex I, III, and IV activities were significantly lower (P < 0.05) in patients than in control subjects. A complex I defect was found in one patient, whereas complex I...

2017
Arun Ghose Christopher M. Taylor Alexander J. Howie Anapurna Chalasani Iain Hargreaves David V. Milford

Background: Mitochondrial disorders can present as kidney disease in children and be difficult to diagnose. Measurement of mitochondrial function in kidney tissue may help diagnosis. This study was to assess the feasibility of obtaining renal samples and analysing them for respiratory chain enzyme activity. Methods: The subjects were children undergoing a routine diagnostic renal biopsy, in who...

Journal: :Human molecular genetics 2006
Marilena D'Aurelio Carl D Gajewski Giorgio Lenaz Giovanni Manfredi

Mitochondrial DNA (mtDNA) mutations cause heterogeneous disorders in humans. MtDNA exists in multiple copies per cell, and mutations need to accumulate beyond a critical threshold to cause disease, because coexisting wild-type mtDNA can complement the genetic defect. A better understanding of the molecular determinants of functional complementation among mtDNA molecules could help us shedding s...

Journal: :PLoS ONE 2008
Paule Bénit Sergio Goncalves Emmanuel Philippe Dassa Jean-Jacques Brière Pierre Rustin

BACKGROUND Despite the considerable progress made in understanding the molecular bases of mitochondrial diseases, no effective treatments have been developed to date. Faithful animal models would be extremely helpful for designing such treatments. We showed previously that the Harlequin mouse phenotype was due to a specific mitochondrial complex I deficiency resulting from the loss of the Apopt...

Journal: :Clinical chemistry 1998
E Ruiz-Pesini C Diez A C Lapeña A Pérez-Martos J Montoya E Alvarez J Arenas M J López-Pérez

Until now, little attention has been paid to the contribution of mitochondrial dysfunction to germinal tissue disorders. The target of this study was to investigate the relationship between sperm motility and mitochondrial respiratory chain enzyme activities. The results obtained showed that semen samples of control individuals (n = 33) have substantially higher activities of complexes I, II, a...

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