نتایج جستجو برای: large granular lymphocyte lgl

تعداد نتایج: 1106700  

Journal: :Blood 2013
Michael J Clemente Bartlomiej Przychodzen Andres Jerez Brittney E Dienes Manuel G Afable Holleh Husseinzadeh Hanna L M Rajala Marcin W Wlodarski Satu Mustjoki Jaroslaw P Maciejewski

New massively parallel sequencing technology enables, through deep sequencing of rearranged T-cell receptor (TCR) Vβ complementarity-determining region 3 (CDR3) regions, a previously inaccessible level of TCR repertoire analysis. The CDR3 repertoire diversity reflects clonal composition, the potential antigenic recognition spectrum, and the quantity of available T-cell responses. In this contex...

Journal: :Blood 2008
Jun Yang P K Epling-Burnette Jeffrey S Painter Jianxiang Zou Fanqi Bai Sheng Wei Thomas P Loughran

Clonal T-cell expansion in patients with T-large-granular lymphocyte (LGL) leukemia occurs by an undefined mechanism that may be related to Fas apoptosis resistance. Here, we demonstrate polarized expansion of CD8(+) terminal-memory differentiation in such patients, as demonstrated by CD45RA expression and absence of CD62L expression, suggesting repeated stimulation by antigen in vivo. Eliminat...

2013
Andres Jerez Michael J. Clemente Hideki Makishima Hanna Rajala Ines Gómez-Seguí Thomas Olson Kathy McGraw Bartlomiej Przychodzen Austin Kulasekararaj Manuel Afable Holleh D. Husseinzadeh Naoko Hosono Francis LeBlanc Sonja Lagström Dan Zhang Pekka Ellonen André Tichelli Catherine Nissen Alan E. Lichtin Aleksandra Wodnar-Filipowicz Ghulam J. Mufti Alan F. List Satu Mustjoki Thomas P. Loughran Jaroslaw P. Maciejewski

Large granular lymphocyte leukemia (LGL) is often associated with immune cytopenias and can co-occur in the context of aplastic anemia (AA) and myelodysplastic syndromes (MDS). We took advantage of the recent description of STAT3 mutations in LGL clonal expansions to test, using sensitive methods, for the presence of these mutations in a large cohort of 367 MDS and 140 AA cases. STAT3 clones ca...

Journal: :Blood 2000
J H Liu S Wei T Lamy P K Epling-Burnette G Starkebaum J Y Djeu T P Loughran

Chronic neutropenia, often associated with rheumatoid arthritis, is a characteristic finding in large granular lymphocyte (LGL) leukemia. The mechanism of neutropenia is not known. Normal neutrophil survival is regulated by the Fas-Fas ligand apoptotic system. We hypothesized that neutropenia in LGL leukemia is mediated by dysregulated expression of Fas ligand. Levels of Fas ligand in serum sam...

Journal: :Blood 1986
V Pistoia E F Prasthofer A B Tilden J C Barton M Ferrarini C E Grossi K Zuckerman

The phenotypic and functional features of purified large granular lymphocytes (LGL) from ten patients with LGL population expansions and cytopenias are described. The predominant LGL phenotypes were T3+, T8+, Leu-11+/-; however, in two patients, LGL expressed a T3-, Leu-11+ phenotype. Variable combinations of other LGL markers (OKM1, Leu-7), and HLA-DR were detected in individual cases. In nine...

Journal: :The Journal of biological chemistry 1989
S Sakamoto J R Ortaldo H A Young

We have evaluated the methylation state of the T cell receptor beta chain gene (TcR beta) in freshly isolated human large granular lymphocyte (LGL) and T cell DNA in order to investigate the relationship between LGL and T cells with regard to methylation of this region of genomic DNA. In addition, we wished to determine whether hypomethylation of specific regions of the beta chain gene DNA migh...

Journal: :Cureus 2023

T-cell large granular lymphocytic (LGL) leukemia is characterized by a clonal proliferation of CD3+ T-cells and has been associated with rheumatoid arthritis (RA). Splenomegaly common finding majority cases present cytopenia. Felty syndrome (FS) neutropenia splenomegaly also classically described in the literature for its association RA. Similarities clinical features, pathogenesis, management,...

2013
E I Andersson H L M Rajala S Eldfors P Ellonen T Olson A Jerez M J Clemente O Kallioniemi K Porkka C Heckman T P Loughran J P Maciejewski S Mustjoki

T-cell large granular lymphocytic (T-LGL) leukemia is a clonal disease characterized by the expansion of mature CD3+CD8+ cytotoxic T cells. It is often associated with autoimmune disorders and immune-mediated cytopenias. Our recent findings suggest that up to 40% of T-LGL patients harbor mutations in the STAT3 gene, whereas STAT5 mutations are present in 2% of patients. In order to identify put...

Journal: :Blood 2004
Marco Herling Joseph D Khoury LaBaron T Washington Madeleine Duvic Michael J Keating Dan Jones

The current World Health Organization (WHO) classification of hematopoietic malignancies defines several types of mature T-cell leukemia including T-cell prolymphocytic leukemia (T-PLL), Sezary syndrome (SS), and T-cell large granular lymphocytic (T-LGL) leukemia. These neoplasms can show overlapping features with each other and with T-cell lymphomas involving peripheral blood (PB). We analyzed...

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