نتایج جستجو برای: ivs4

تعداد نتایج: 128  

Journal: :The Turkish journal of pediatrics 2016
Birgül Kırel Meliha Demiral Özkan Bozdağ Kadri Karaer

Pseudohypoparathyroidism (PHP) type Ia is characterized by multiple hormone resistance; primarily parathyroid hormone (PTH) resistance and Albright's hereditary osteodystrophy (AHO) which involves skeletal and developmental defects. The AHO phenotype alone without hormone resistance is defined as pseudoPHP. A boy was first diagnosed as having both rickets and primary hypothyroidism at 2.5 month...

Journal: :Arteriosclerosis and thrombosis : a journal of vascular biology 1994
J Emmerich D Vidaud M Alhenc-Gelas G Chadeuf M Gouault-Heilmann M F Aillaud M Aiach

We have identified three novel mutations of the antithrombin (AT) gene in patients with thrombotic complications: a Cys 128 --> Tyr mutations, a G --> A mutation in the intervening sequence 4 (IVS4) 14 nucleotide 5' to exon 5, and a 9 bp deletion in the 3' end of exon 6 resulting in a short aberrant sequence after Arg 425. The latter mutation was associated with an Arg 47 --> His mutation in tw...

2009
VICTORIA E. PARERA RITA H. KOOLE GARDI MINDERMAN ANNIE EDIXHOVEN MARIA V. ROSSETTI ALCIRA BATLLE FELIX.W.M DE ROOIJ José de San Martín

Erythropoietic Protoporphyria (EPP) is an inherited disorder of porphyrin metabolism in which decreased activity of ferrochelatase (FECH) leads to accumulation of protoporphyrin IX (PP IX) in red blood cells, plasma, liver, bile and increased excretion in feces. Clinically, EPP is characterized by photosensitivity that includes burning, swelling, itching and painful erythema in sun exposed area...

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