نتایج جستجو برای: idiopathic pulmonary arterial hypertension ipah

تعداد نتایج: 480229  

Journal: :American journal of physiology. Cell physiology 2014
Shanshan Song Aya Yamamura Hisao Yamamura Ramon J Ayon Kimberly A Smith Haiyang Tang Ayako Makino Jason X-J Yuan

An increase in cytosolic Ca(2+) concentration ([Ca(2+)]cyt) in pulmonary arterial smooth muscle cells (PASMC) is a major trigger for pulmonary vasoconstriction and an important stimulus for pulmonary arterial medial hypertrophy in patients with idiopathic pulmonary arterial hypertension (IPAH). Vascular smooth muscle cells (SMC) sense the blood flow shear stress through interstitial fluid drive...

Journal: :American journal of respiratory and critical care medicine 2006
Elisabeth D Willers John H Newman James E Loyd Ivan M Robbins Lisa A Wheeler Melissa A Prince Krista C Stanton Joy A Cogan James R Runo Daniel Byrne Marc Humbert Gerald Simonneau Benjamin Sztrymf Jane A Morse James A Knowles Kari E Roberts Jude J McElroy Robyn J Barst John A Phillips

RATIONALE Serotonin is a pulmonary vasoconstrictor and smooth muscle cell mitogen. The serotonin transporter (SERT) is abundant in pulmonary vascular smooth muscle. Compared with the short (S) allele, the long (L) SERT promoter allele is associated with increased SERT transcription and more severe pulmonary hypertension in a cohort of patients with chronic obstructive pulmonary disease, and was...

2017
Kasper Hasseriis Andersen Claus Bøgelund Andersen Finn Gustafsson Jørn Carlsen

Pulmonary vascular arterial remodeling is an integral and well-understood component of pulmonary hypertension (PH). In contrast, morphological alterations of pulmonary veins in PH are scarcely described. Explanted lungs (n = 101) from transplant recipients with advanced chronic obstructive pulmonary disease (COPD) and idiopathic pulmonary arterial hypertension (IPAH) were analyzed for venous va...

2017
Cathelijne E. van der Bruggen Onno A. Spruijt Esther J. Nossent Pia Trip J. Tim Marcus Frances S. de Man Harm Jan Bogaard Anton Vonk Noordegraaf

Patients with idiopathic pulmonary arterial hypertension (IPAH) and a reduced diffusion capacity of the lung for carbon monoxide (DLCO) have a worse survival compared to IPAH patients with a preserved DLCO. Whether this poor survival can be explained by unresponsiveness to pulmonary hypertension (PH)-specific vasodilatory therapy is unknown. Therefore, the aim of this study was to evaluate the ...

Journal: :American journal of physiology. Heart and circulatory physiology 2006
Jan-Willem Lankhaar Nico Westerhof Theo J C Faes Koen M J Marques J Tim Marcus Piet E Postmus Anton Vonk-Noordegraaf

Right ventricular (RV) afterload is commonly defined as pulmonary vascular resistance, but this does not reflect the afterload to pulsatile flow. The purpose of this study was to quantify RV afterload more completely in patients with and without pulmonary hypertension (PH) using a three-element windkessel model. The model consists of peripheral resistance (R), pulmonary arterial compliance (C),...

Journal: :The European respiratory journal 2012
Mark Toshner Jay Suntharalingam Pierre Fesler Elaine Soon Karen K Sheares David Jenkins Paul White Nicholas W Morrell Robert Naeije Joanna Pepke-Zaba

Flow-directed pulmonary artery occlusion is posited to enable partitioning of vascular resistance into small and large vessels. As such it may have a role in assessment for pulmonary endarterectomy. To test if the occlusion technique distinguished small from large vessel disease we studied 59 subjects with chronic thromboembolic pulmonary hypertension (CTEPH), idiopathic pulmonary arterial hype...

2014
J. K. Mansoor Edward S. Schelegle Cristina E. Davis William F. Walby Weixiang Zhao Alexander A. Aksenov Alberto Pasamontes Jennifer Figueroa Roblee Allen

BACKGROUND An important challenge to pulmonary arterial hypertension (PAH) diagnosis and treatment is early detection of occult pulmonary vascular pathology. Symptoms are frequently confused with other disease entities that lead to inappropriate interventions and allow for progression to advanced states of disease. There is a significant need to develop new markers for early disease detection a...

2011
Livia Kapusta

Background—Incidence and prevalence rates for pediatric pulmonary hypertension (PH) and pulmonary arterial hypertension (PAH) are unknown. This study describes the nationwide epidemiological features of pediatric PH in the Netherlands during a 15-year period and the clinical course of pediatric PAH. Methods and Results—Two registries were used to retrospectively identify children (0–17 years) w...

Journal: :Journal of the American College of Cardiology 2007
Xing-Xiang Wang Fu-Rong Zhang Yun-Peng Shang Jun-Hui Zhu Xu-Dong Xie Qian-Min Tao Jian-Hua Zhu Jun-Zhu Chen

OBJECTIVES The goal of this study was to investigate the feasibility, safety, and initial clinical outcome of intravenous infusion of autologous endothelial progenitor cells (EPCs) in patients with idiopathic pulmonary arterial hypertension (IPAH). BACKGROUND Experimental data suggest that transplantation of EPCs attenuates monocrotaline-induced pulmonary hypertension in rats and dogs. In add...

Journal: :Respiration; international review of thoracic diseases 2008
Silvia Ulrich Mark R Nicolls Laima Taraseviciene Rudolf Speich Norbert Voelkel

BACKGROUND An association between pulmonary arterial hypertension (PAH) and various immune disorders is well established. Recently, the role of an intact immune system in protecting against pulmonary angioproliferation was shown in an animal model. OBJECTIVE To elucidate the role of T cells in human PAH, we comparatively studied T cell subclasses with emphasis on regulatory T cells (T(reg)) i...

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