نتایج جستجو برای: heteroplasmy

تعداد نتایج: 700  

Journal: :Canadian Journal of Neurological Sciences 2022

Background: MT-TA (OMIM 590000), one of 22 mitochondrial transfer-RNA (mt-tRNA) genes, encodes the mt-tRNA for alanine. Pathogenic variants in genes affect translation respiratory chain complexes I, III, and IV; which leads to dysfunction a clinically variable phenotype. pathogenic have been described only seven patients, all whom had isolated myopathy Methods: Case report. Results: Our patient...

2012
Hui-Ting Lee Chen-Sung Lin Wei-Sheng Chen Hsien-Tzung Liao Chang-Youh Tsai Yau-Huei Wei

The role of mitochondrial DNA (mtDNA) alterations in the pathophysiology of systemic lupus erythematosus (SLE) remains unclear. We investigated sequence variations in the D310 region and copy number change of mtDNA in 85 SLE patients and 45 normal subjects. Leukocyte DNA and RNA were extracted from leukocytes of the peripheral venous blood. The D310 sequence variations and copy number of mtDNA,...

Journal: :Forensic science international 2002
Antonio Alonso Antonio Salas Cristina Albarrán Eduardo Arroyo Azucena Castro Manuel Crespillo Ana María di Lonardo María Victoria Lareu Carlos López Cubría Manuel López Soto José A Lorente Marta Montesino Semper Ana Palacio Manuel Paredes Luisa Pereira Anna Pérez Lezaun José Pestano Brito Andrea Sala María Conceiçao Vide Martín Whittle Juan J Yunis Josefina Gómez

The Spanish and Portuguese working group (GEP) of international society for forensic genetics (ISFG) 1999-2000 collaborative exercise on mitochondrial DNA (mtDNA) included the analysis of four bloodstain samples and one hair shaft sample by 19 participating laboratories from Spain, Portugal and several Latin-American countries. A wide range of sequence results at position 16,093 of the HV1 (fro...

2016
Yuexiao Qi Yuehua Wei Qiaoli Wang Hui Xu You Wang Anqi Yao Hui Yang Yan Gao Fuxiang Zhou

Mitochondrial dysfunction is associated with pathogenic mitochondrial (mt)DNA mutations. The majority of mtDNA point mutations have a heteroplasmic status, which is defined as the coexistence of wild-type and mutated DNA within a cell or tissue. Previous findings demonstrated that certain mtDNA heteroplasmic mutations contribute to widely spread chronic diseases, including cancer, and alteratio...

Journal: :Genetics 1998
R K Chesser

This study assesses factors that influence the rates of change of organelle gene diversity and the maintenance of heteroplasmy. Losses of organelle gene diversity within individuals via vegetative segregation during ontogeny are paramount to resultant spatial and temporal patterns. Steady-state losses of organelle variation from the zygote to the gametes are determined by the effective number o...

Journal: :Cloning and stem cells 2007
Christina Ramires Ferreira Flávio Vieira Meirelles Walt Yamazaki Marcos Roberto Chiaratti Simone Cristina Méo Felipe Perecin Lawrence Charles Smith Joaquim Mansano Garcia

The mechanisms controlling the outcome of donor cell-derived mitochondrial DNA (mtDNA) in cloned animals remain largely unknown. This research was designed to investigate the kinetics of somatic and embryonic mtDNA in reconstructed bovine embryos during preimplantation development, as well as in cloned animals. The experiment involved two different procedures of embryo reconstruction and their ...

Journal: :Proceedings of the National Academy of Sciences 1983

2016
Riana I. Wernick Suzanne Estes Dana K. Howe Dee R. Denver

Heteroplasmy-the presence of more than one mitochondrial DNA (mtDNA) sequence type in a cell, tissue, or individual-impacts human mitochondrial disease and numerous aging-related syndromes. Understanding the trans-generational dynamics of mtDNA is critical to understanding the underlying mechanisms of mitochondrial disease and evolution. We investigated mtDNA mutation and heteroplasmy using a s...

Journal: :Seminars in Cell & Developmental Biology 2020

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