Didelphic uterus with obstructed hemivagina and ipsilateral renal agenesis is a rare condition. It usually presents with pelvic pain following the menarche, dysmenorrhoea, and an increase in abdominal volume or a palpable mass due to unilateral haematocolpos. We present the case of a 13-year-old girl who referred with recurrent pelvic pain, mainly at the time of menses, and irregular menstrual ...

Genital outflow tract obstruction is a rare cause of primary amenorrhea. A transverse vaginal septum is a defect of vertical fusion between the para-mesonephric ducts and uro-genital sinus. If the septum is complete, the menstrual flow will be obstructed causing primary amenorrhea. The septum is basically a membrane of fibrous connective tissue with both vascular and muscular components formed ...

Background: Mostyn Embrey syndrome is a rare disorder associated with unilateral renal agenesis and malformations of the female reproductive tract. Delayed diagnosis is associated with serious diagnostic difficulties that may lead to inappropriate management including harmful surgery. Aim: The aim of this paper is to describe the first case of this rare syndrome in Iraq and, and to make a recom...

STUDY OBJECTIVE To study clinical features of patient presented with severe hydramnios, associated with hydronephrosis, that was antenatally diagnosed and has been successfully treated immediately after birth. At a molecular level, we investigated the gene expression of key steroidogenic enzymes from the maternal ovary. DESIGN Ultrasound scan, MRI, semi-quantitative RT-PCR SETTING: The patien...

Obstructed hemivagina and ipsilateral renal anomaly (OHVIRA), also known as Herlyn-Werner-Wunderlich syndrome, is a rare syndrome with only a few hundred reported cases described since 1922. Only a handful of these cases have been associated with pyocolpos. Mullerian duct anomalies have an incidence of 2-3%. While OHVIRA constitutes 0.16-10% of these Mullerian duct anomalies. Symptoms usually p...

Background: Amenorrhea is defined as the absence of menarche in females reproductive age. Primary amenorrhea failure to reach by age 13 with no secondary sexual characteristics if has not occurred five years after initial breast development or patient 15 older. A transverse vaginal septum a rare congenital abnormality Mullerian duct that can cause primary amenorrhea. Transverse incidence ranges...

PURPOSE Genital reconstruction in female patients with virilizing congenital adrenal hyperplasia (CAH) is very challenging. Our aim was to evaluate the techniques employed to treat complications after failure of primary urogenital sinus (UGS) surgery, as well as the result of these reoperations. PATIENTS AND METHODS Twenty girls with virilizing CAH who were previously submitted to genitoplast...