نتایج جستجو برای: dystrophic epidermolysis bullosa

تعداد نتایج: 6516  

Journal: :Archives of disease in childhood 2005
S M Taibjee P Ramani R Brown C Moss

There are previous reports of dilated cardiomyopathy (DCM) in recessive dystrophic epidermolysis bullosa (RDEB), a debilitating blistering skin disorder. The pathogenesis of DCM in RDEB remains uncertain, although dietary deficiency of selenium and carnitine have been implicated. A 6 year old girl with RDEB who died of DCM is reported; attention is drawn to the possible role of two potentially ...

Journal: :Archives of dermatology 2004
Marvin J Rapaport Vicki H Rapaport

1. Wagner JD, Evdokimow DZ, Weisberger E, et al. Sentinel node biopsy for highrisk nonmelanoma cutaneous malignancy. Arch Dermatol. 2004;140:75-79. 2. Fine JD, Johnson LB, Suchindran C, et al. Cancer and inherited epidermolysis bullosa: lifetable analyses of the National Epidermolysis Bullosa Registry study population. In: Fine JD, Bauer EA, McGuire J, Moshell A, eds. Epidermolysis Bullosa: Cli...

Journal: :Anais brasileiros de dermatologia 2011
Juliana Nakano de Melo Priscila Yoshie Teruya Maria Cecília Rivitti Machado Neusa Sakai Valente Mirian Nacagami Sotto Zilda Najjar Prado de Oliveira

Acquired melanocytic lesions may present unusual clinical features in all forms of hereditary epidermolysis bullosa. These lesions are known as "EB nevi", and often pose a diagnostic challenge for dermatologists given their resemblance - clinically, dermoscopically and histologically - to melanoma. The lesions have been reported in all types of hereditary EB, most of them in childhood. We repor...

Journal: :Archives of disease in childhood 2000
R U Sidwell R Yates D Atherton

BACKGROUND Dystrophic epidermolysis bullosa (DEB) is an uncommon genetic disorder of the skin and mucosae. In 1996, we reported the occurrence of lethal dilated cardiomyopathy (DCM) in two affected children. METHODS In the past seven years we have routinely screened patients with severe DEB who have been under the care of this hospital by yearly clinical review, echocardiography, and quantifi...

Journal: :Journal of the American College of Cardiology 2013

Journal: :Nihon Naibunpi Gakkai zasshi 1990
F Nakamura H Rakugi K Fukuo M Nakamaru F Masugi T Onishi T Ogihara K Hashimoto T Kozuka K Yoshikawa

Epidermolysis bullosa is a group of disorders whose common primary feature is the formation of blisters following trivial trauma. Recessive dystrophic epidermolysis bullosa (RDEB), a subtype of epidermolysis bullosa, is frequently associated with growth retardation. This growth retardation has been reported to be caused by trophopathy following protein loss through skin lesions. Endocrine disor...

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