Patients with congenital heart disease corrected in early childhood may later in life present with cardiac symptoms caused by other associated congenital anomalies that were initially not diagnosed. Nowadays, several noninvasive imaging modalities are available for the visualisation of cardiac anatomy in great detail. We describe two patients with an unroofed coronary sinus, a rare congenital a...

Agenesis of the ductus arteriosus is a rare congenital cardiac anomaly which should be considered within the differntial prenatal diagnosis of hydrops fetalis.

DURING the past decade definite progress has been made toward an understanding of the hemodynamic alterations and pathophysiologic aspects of Ebstein's anomaly of the tricuspid valve.1' 2 Moreover, an increased awareness of the characteristic clinical findings has resulted in an apparent increase in incidence of the disease. Largely as a result of careful pathologic studies, atypical forms of E...

DURING the past decade definite progress has been made toward an understanding of the hemodynamic alterations and pathophysiologic aspects of Ebstein's anomaly of the tricuspid valve.1' 2 Moreover, an increased awareness of the characteristic clinical findings has resulted in an apparent increase in incidence of the disease. Largely as a result of careful pathologic studies, atypical forms of E...

Background: The most common congenital abnormality of esophagus is esophageal atresia (EA) that can occur with or without tracheoesophageal fistula. Other associated anomalies are the leading cause of death in these patients. The present study aimed to evaluate the main complication, outcomes and cause of death in neonate with EA repaired in Amirkola Children’s Hospital (ACH), Iran within...

BACKGROUND Left coronary artery arising from the right sinus of Valsalva is an uncommon congenital coronary anomaly that seems to be associated with sudden death in young patients. CASE PRESENTATION We report a case of cardiac arrest in a 59-year-old patient after sexual intercourse and Sildenafil ingestion. A coronary arteriography and an angiographic computed tomography scan subsequently re...

BACKGROUND Double-orifice mitral valve is an extremely rare cardiac anomaly possibly originating from insufficient endocardial fusion in embryogenesis. Severe concomitant cardiac anomalies and malfunction of the valve usually lead to an early diagnosis in childhood. Therefore the prevalence of isolated double-orifice mitral valve in adulthood is not known. CASE PRESENTATION We present the cas...

E BSTEIN’S ANOMALY, FIRST DESCRIBED in 1866, is relatively rare. It is a downward displacement of the tricuspid (right atrioventricular) valve below its annulus, dividing the right heart into a relatively large atrium and a small, at times functionless, right ventricle. The foramen ovale is usually patent and there may be other intracardiac anomalies.” We are describing a similar lesion involvi...