نتایج جستجو برای: bifid uvula

تعداد نتایج: 1243  

2017
Rafael Santiago de Almeida Willian Caetano Rodrigues Willian Morais de Melo Juliana Seo Hitoshi Shinohara

Seventeen-year-old female patient was evaluated with the complaint of pit-shaped injury located in semi lower lip mucosa, since birth, and there was no salivary secretion. During the intra oral examination, bifid uvula was noted, others mucous membranes showed normal aspects of coloration and texture and teeth were in excellent conditions of hygiene and conservation. It was asymptomatic and the...

Journal: :Romanian journal of morphology and embryology = Revue roumaine de morphologie et embryologie 2010
Andrada Soancă Diana Dudea H Gocan Alexandra Roman B Culic

BACKGROUND The present paper describes the oral manifestations in a 16-year-old boy previously diagnosed with Apert syndrome. PATIENT AND METHODS The extraoral and intraoral pathological findings were recorded. The following intraoral parameters were recorded: plaque and calculus deposits, dental caries, periodontal status, malpositions, and occlusion. For the upper anterior teeth, dental sha...

2014
Marjolijn Renard Bram Trachet Christophe Casteleyn Laurence Campens Pieter Cornillie Bert Callewaert Steven Deleye Bert Vandeghinste Paula M. van Heijningen Harry Dietz Filip De Vos Jeroen Essers Steven Staelens Patrick Segers Bart Loeys Paul Coucke Anne De Paepe Julie De Backer

Loeys-Dietz syndrome (LDS) is an autosomal dominant arterial aneurysm disease belonging to the spectrum of transforming growth factor β (TGFβ)-associated vasculopathies. In its most typical form it is characterized by the presence of hypertelorism, bifid uvula/cleft palate and aortic aneurysm and/or arterial tortuosity. LDS is caused by heterozygous loss of function mutations in the genes encod...

Journal: :The Turkish journal of pediatrics 2012
Esra Kiliç Yasemin Alanay Eda Utine Burçe Ozgen-Mocan Peter N Robinson Koray Boduroğlu

We report a 13-year-old girl with Loeys-Dietz syndrome (LDS) caused by a known transforming growth factor beta receptor II (TGFBR2) gene mutation, who developed aortic root dilatation and saccular aneurysm of the internal carotid artery. LDS is a rare, autosomal dominant aortic aneurysm syndrome with multisystem involvement. The disease is typically characterized by the triad of arterial tortuo...

Journal: :Journal of medical genetics 1988
G N Wilson W J Oliver

Three families including five subjects with the G or Opitz-Frias syndrome are added to 23 published cases who had dysphagia; characteristics of the two affected relatives were added to 19 well documented published reports. The data from index cases support the concept of the G syndrome as a constellation of midline defects, which include hypertelorism or telecanthus (89%), oesophageal dysmotili...

Journal: :BMJ case reports 2013
Ravi Prakash Sasankoti Mohan Sankalp Verma Amit Singh Udita Singh

To cite: Mohan RPS, Verma S, Singh A, et al. BMJ Case Rep Published online: [please include Day Month Year] doi:10.1136/ bcr-2013-008664 DESCRIPTION A 57-year-old man reported to the outpatient department with the chief compliant of deformed upper lip which was present since birth. He denied any complaints other than cosmetic ones. On examination, an extra fold of redundant tissue was present o...

Journal: :Middle East journal of anaesthesiology 2016
Judy G Johnson Jacob P Bray William H Risher Alan David Kaye

Loeys-Dietz syndrome (LDS) is a rare autosomal dominant disease related to genetic mutations in receptors for the cytokine transforming growth factor-receptor type 1 (TGFB-R1) or 2 gene (TGFB-R2) on the cell surface. LDS results in abnormal protein synthesis and dysfunctional connective tissue, which can result in unique cardiovascular anesthesia challenges related to perioperative management. ...

Journal: :British heart journal 1984
Y Watanabe H Toda M Nishimura

In 129 electrocardiograms from 129 patients showing bifid T waves as well as U waves the intervals from the beginning of the QRS complex to the two T wave apices (QaT1, QaT2), to the end of the T wave (QeT), and to the apex of the U wave (QaU) were measured. Eighty additional electrocardiograms from matched control subjects showing single peaked T waves were also studied. The precordial distrib...

Journal: :The Lancet 1841

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