Results Fifty six patients were included: 17 CAPS, 4 TRAPS, 5 HIDS, 18 FMF, 6 CRMO, 2 SAPHO and 4 Behcet. The median follow-up period was 2 years (0-14 years). The male/female ratio was 20/36. The median age was 2.5 years at disease onset and 4 years at diagnosis. Family history was positive in 34% of patients. Clinical manifestations included fever (79%), mucocutaneous (61%), musculoskeletal (...

introduction: behcet's disease is a chronic disease with multisystem involvement characterized clinically by oral and genital aphthae, cutaneous lesions and ophthalmologic, neurologic and gastrointestinal manifestation. nervous system involvement occurs in 5.3 – 30% of patients, mostly in brain stem and basal ganglia. the common manifestations are pyramidal signs, central nervous plegia, p...

Yeşim Oymak1, Bülent Güzel2, Hüseyin Gümüş2, Erdem Dağlıoğlu3, Ali Ayçiçek2, Ahmet Koç2, Derya Özyürük4 1Dr. Behçet Uz Children’s Hospital, Clinic of Hematology, İzmir, Turkey 2Harran University Faculty of Medicine, Department of Pediatric Hematology, Şanlıurfa, Turkey 3Harran University Faculty of Medicine, Department of Radiology, Şanlıurfa, Turkey 4Şanlıurfa Children’s Hospital, Clinic of Pe...

KEY CLINICAL MESSAGE Behcet's disease (BD) is a rare condition which is diagnosed clinically. Only few cases have been reported in sub-Saharan Africa. We report a Tanzanian male who presented with typical features of BD and was successfully treated. There should be an increase in awareness on BD to improve the management.

purpose : to investigate the risk factors and causes for blindness in behcet’s disease (bd). methods : in this preliminary retrospective case series we have investigated 27 bd patients (54 eyes), legally blind (vision 0.1 or less) at least in one eye at the last visit (2006), and compared them with 54 eyes of 27 non-blind patients (control group), matched individually and consequently in terms ...

Methods A retrospective study was made of 6 consecutive pediatric patients with Behçet disease. Inclusion criteria were fulfillment of the classification criteria of the International Study Group for Behçet Disease and onset of uveitis at 16 years of age or younger. The main outcome measures were sex, age at onset of uveitis, the initial symptom of Behcet disease, clinical ocular features, ocul...

Behcet disease (BD), a vasculitic disease, may present with a broad range of systemic manifestations. Urologic complications are rarely described in the literature, but when they occur, they present as epididymo-orchitis. We describe a rare case of testicular infarction in a patient with BD followed up with serial ultrasound imaging. We highlight the diagnostic challenges when presented with te...